Your browser doesn't support javascript.
loading
Elesclomol alleviates Menkes pathology and mortality by escorting Cu to cuproenzymes in mice.
Guthrie, Liam M; Soma, Shivatheja; Yuan, Sai; Silva, Andres; Zulkifli, Mohammad; Snavely, Thomas C; Greene, Hannah Faith; Nunez, Elyssa; Lynch, Brogan; De Ville, Courtney; Shanbhag, Vinit; Lopez, Franklin R; Acharya, Arjun; Petris, Michael J; Kim, Byung-Eun; Gohil, Vishal M; Sacchettini, James C.
Afiliação
  • Guthrie LM; Department of Molecular and Cellular Medicine, Texas A&M Health Science Center, College Station, TX 77843, USA.
  • Soma S; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Yuan S; Department of Animal and Avian Sciences, University of Maryland, College Park, MD 20742, USA.
  • Silva A; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Zulkifli M; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Snavely TC; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Greene HF; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Nunez E; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Lynch B; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • De Ville C; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Shanbhag V; Department of Biochemistry, University of Missouri, Columbia, MO 65211, USA.
  • Lopez FR; Texas Veterinary Medicine Diagnostic Laboratory, College Station, TX 77843, USA.
  • Acharya A; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA.
  • Petris MJ; Department of Biochemistry, University of Missouri, Columbia, MO 65211, USA.
  • Kim BE; Department of Animal and Avian Sciences, University of Maryland, College Park, MD 20742, USA.
  • Gohil VM; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA. vgohil@tamu.edu sacchett@tamu.edu.
  • Sacchettini JC; Department of Biochemistry and Biophysics, Texas A&M University, College Station, TX 77843, USA. vgohil@tamu.edu sacchett@tamu.edu.
Science ; 368(6491): 620-625, 2020 05 08.
Article em En | MEDLINE | ID: mdl-32381719

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Cobre / Hidrazinas / Síndrome dos Cabelos Torcidos Limite: Animals Idioma: En Revista: Science Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Estados Unidos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Cobre / Hidrazinas / Síndrome dos Cabelos Torcidos Limite: Animals Idioma: En Revista: Science Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Estados Unidos