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Medical nutrition therapy in patients with HIBCH and ECHS1 defects: Clinical and biochemical response to low valine diet.
Abdenur, J E; Sowa, M; Simon, M; Steenari, M; Skaar, J; Eftekharian, S; Chang, R; Ferdinandusse, S; Pitt, J.
Afiliação
  • Abdenur JE; Division of Metabolic Disorders, CHOC Children's, Orange, CA, USA.
  • Sowa M; Department of Pediatrics, University of California Irvine, Orange, CA. USA.
  • Simon M; Division of Metabolic Disorders, CHOC Children's, Orange, CA, USA.
  • Steenari M; Division of Metabolic Disorders, CHOC Children's, Orange, CA, USA.
  • Skaar J; Division of Neurology, CHOC Children's. Orange, CA, USA.
  • Eftekharian S; Department of Pediatrics, University of California Irvine, Orange, CA. USA.
  • Chang R; Division of Metabolic Disorders, CHOC Children's, Orange, CA, USA.
  • Ferdinandusse S; Division of Metabolic Disorders, CHOC Children's, Orange, CA, USA.
  • Pitt J; Division of Metabolic Disorders, CHOC Children's, Orange, CA, USA.
Mol Genet Metab Rep ; 24: 100617, 2020 Sep.
Article em En | MEDLINE | ID: mdl-32642440

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Mol Genet Metab Rep Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Estados Unidos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Mol Genet Metab Rep Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Estados Unidos