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Increased protein propionylation contributes to mitochondrial dysfunction in liver cells and fibroblasts, but not in myotubes.
Lagerwaard, Bart; Pougovkina, Olga; Bekebrede, Anna F; Te Brinke, Heleen; Wanders, Ronald J A; Nieuwenhuizen, Arie G; Keijer, Jaap; de Boer, Vincent C J.
Afiliação
  • Lagerwaard B; Human and Animal Physiology, Wageningen University and Research, Wageningen, Netherlands.
  • Pougovkina O; TI Food and Nutrition, Wageningen, Netherlands.
  • Bekebrede AF; Laboratory Genetic Metabolic Diseases, Department of Clinical Chemistry, Academic Medical Center, University of Amsterdam, Amsterdam, Netherlands.
  • Te Brinke H; Human and Animal Physiology, Wageningen University and Research, Wageningen, Netherlands.
  • Wanders RJA; Laboratory Genetic Metabolic Diseases, Department of Clinical Chemistry, Academic Medical Center, University of Amsterdam, Amsterdam, Netherlands.
  • Nieuwenhuizen AG; Laboratory Genetic Metabolic Diseases, Department of Clinical Chemistry, Academic Medical Center, University of Amsterdam, Amsterdam, Netherlands.
  • Keijer J; Department of Pediatrics, Emma Children's Hospital, Academic Medical Center, University of Amsterdam, Amsterdam, Netherlands.
  • de Boer VCJ; Human and Animal Physiology, Wageningen University and Research, Wageningen, Netherlands.
J Inherit Metab Dis ; 44(2): 438-449, 2021 03.
Article em En | MEDLINE | ID: mdl-32740932

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fibras Musculares Esqueléticas / Metilmalonil-CoA Descarboxilase / Acidemia Propiônica / Fibroblastos / Mitocôndrias Limite: Humans Idioma: En Revista: J Inherit Metab Dis Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Holanda

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fibras Musculares Esqueléticas / Metilmalonil-CoA Descarboxilase / Acidemia Propiônica / Fibroblastos / Mitocôndrias Limite: Humans Idioma: En Revista: J Inherit Metab Dis Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Holanda