The systemic autoinflammatory disorders for dermatologists. Part 2: disease examples.
Clin Exp Dermatol
; 45(8): 967-973, 2020 Dec.
Article
em En
| MEDLINE
| ID: mdl-32882069
ABSTRACT
The systemic autoinflammatory disorders (SAIDS) or periodic fever syndromes are disorders of innate immunity, which can be inherited or acquired. They are almost all very rare and easily overlooked; typically, patients will have seen multiple specialities prior to diagnosis, so a high level of clinical suspicion is key. It is important to note that these are 'high-value' diagnoses as the majority of these syndromes can be very effectively controlled, dramatically improving quality of life and providing protection against the development of irreversible complications such as AA amyloidosis. In Part 1 of this review, we took an overview of SAIDS and described the common features; in this article, we take a more in-depth look at the better recognized or more dermatologically relevant conditions.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Receptores de Interleucina-1
/
Doenças Hereditárias Autoinflamatórias
/
Dermatologistas
/
Amiloidose
/
Doenças do Sistema Imunitário
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
Idioma:
En
Revista:
Clin Exp Dermatol
Ano de publicação:
2020
Tipo de documento:
Article
País de afiliação:
Reino Unido