Impact of sodium phenylbutyrate treatment in acute management of maple syrup urine disease attacks: a single-center experience.

Zubarioglu, Tanyel; Dede, Elif; Cigdem, Humeyra; Kiykim, Ertugrul; Cansever, Mehmet S; Aktuglu-Zeybek, Cigdem

Zubarioglu, Tanyel; Dede, Elif; Cigdem, Humeyra; Kiykim, Ertugrul; Cansever, Mehmet S; Aktuglu-Zeybek, Cigdem.

Afiliação

Zubarioglu T; Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Pediatrics Division of Nutrition and Metabolism, Istanbul, Turkey.
Dede E; Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Pediatrics, Istanbul, Turkey.
Cigdem H; Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Pediatrics Division of Nutrition and Metabolism, Istanbul, Turkey.
Kiykim E; Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Pediatrics Division of Nutrition and Metabolism, Istanbul, Turkey.
Cansever MS; Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Central Laboratory, Istanbul, Turkey.
Aktuglu-Zeybek C; Istanbul University-Cerrahpasa, Cerrahpasa Medical Faculty, Department of Pediatrics Division of Nutrition and Metabolism, Istanbul, Turkey.

J Pediatr Endocrinol Metab ; 34(1): 121-126, 2021 Jan 27.

Article em En | MEDLINE | ID: mdl-33180043

Assuntos

Antineoplásicos/uso terapêutico; Doença da Urina de Xarope de Bordo/tratamento farmacológico; Fenilbutiratos/uso terapêutico; Criança; Pré-Escolar; Gerenciamento Clínico; Feminino; Seguimentos; Humanos; Lactente; Masculino; Doença da Urina de Xarope de Bordo/patologia; Prognóstico; Estudos Retrospectivos

Palavras-chave

CRRT; MSUD; emergency treatment; extracorporeal toxin removal; sodium phenylbutyrate

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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fenilbutiratos / Doença da Urina de Xarope de Bordo / Antineoplásicos Tipo de estudo: Observational_studies / Prognostic_studies Limite: Child / Child, preschool / Female / Humans / Infant / Male Idioma: En Revista: J Pediatr Endocrinol Metab Assunto da revista: ENDOCRINOLOGIA / PEDIATRIA Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Turquia

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