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Effect of CFTR correctors on the traffic and the function of intracellularly retained ABCB4 variants.
Ben Saad, Amel; Vauthier, Virginie; Tóth, Ágota; Janaszkiewicz, Angelika; Durand-Schneider, Anne-Marie; Bruneau, Alix; Delaunay, Jean-Louis; Lapalus, Martine; Mareux, Elodie; Garcin, Isabelle; Gonzales, Emmanuel; Housset, Chantal; Aït-Slimane, Tounsia; Jacquemin, Emmanuel; Di Meo, Florent; Falguières, Thomas.
Afiliação
  • Ben Saad A; Inserm, Université Paris-Saclay, Physiopathogénèse et traitement des maladies du foie, UMR_S 1193, Orsay, France.
  • Vauthier V; Inserm, Sorbonne Université, Centre de Recherche Saint-Antoine (CRSA), UMR_S 938, Institute of Cardiometabolism and Nutrition (ICAN), Paris, France.
  • Tóth Á; Inserm, Sorbonne Université, Centre de Recherche Saint-Antoine (CRSA), UMR_S 938, Institute of Cardiometabolism and Nutrition (ICAN), Paris, France.
  • Janaszkiewicz A; Université de Paris, Institut Cochin, Inserm U1016, CNRS UMR 8104, Paris, France.
  • Durand-Schneider AM; Inserm, Université de Limoges, UMR 1248 IPPRITT, Limoges, France.
  • Bruneau A; Inserm, Université de Limoges, UMR 1248 IPPRITT, Limoges, France.
  • Delaunay JL; Inserm, Sorbonne Université, Centre de Recherche Saint-Antoine (CRSA), UMR_S 938, Institute of Cardiometabolism and Nutrition (ICAN), Paris, France.
  • Lapalus M; Inserm, Sorbonne Université, Centre de Recherche Saint-Antoine (CRSA), UMR_S 938, Institute of Cardiometabolism and Nutrition (ICAN), Paris, France.
  • Mareux E; Department of Hepatology & Gastroenterology, Charité Universitätsmedizin Berlin, Berlin, Germany.
  • Garcin I; Inserm, Sorbonne Université, Centre de Recherche Saint-Antoine (CRSA), UMR_S 938, Institute of Cardiometabolism and Nutrition (ICAN), Paris, France.
  • Gonzales E; Inserm, Université Paris-Saclay, Physiopathogénèse et traitement des maladies du foie, UMR_S 1193, Orsay, France.
  • Housset C; Inserm, Université Paris-Saclay, Physiopathogénèse et traitement des maladies du foie, UMR_S 1193, Orsay, France.
  • Aït-Slimane T; Inserm, Université Paris-Saclay, Physiopathogénèse et traitement des maladies du foie, UMR_S 1193, Orsay, France.
  • Jacquemin E; Inserm, Université Paris-Saclay, Physiopathogénèse et traitement des maladies du foie, UMR_S 1193, Orsay, France.
  • Di Meo F; Assistance Publique - Hôpitaux de Paris, CHU Bicêtre, Paediatric Hepatology & Paediatric Liver Transplant Department, Reference Center for Rare Paediatric Liver Diseases, FILFOIE, ERN Rare-Liver, Faculté de Médecine Paris-Saclay, Le Kremlin-Bicêtre, France.
  • Falguières T; Inserm, Sorbonne Université, Centre de Recherche Saint-Antoine (CRSA), UMR_S 938, Institute of Cardiometabolism and Nutrition (ICAN), Paris, France.
Liver Int ; 41(6): 1344-1357, 2021 06.
Article em En | MEDLINE | ID: mdl-33650203

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Colestase / Colestase Intra-Hepática Limite: Humans Idioma: En Revista: Liver Int Assunto da revista: GASTROENTEROLOGIA Ano de publicação: 2021 Tipo de documento: Article País de afiliação: França

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Colestase / Colestase Intra-Hepática Limite: Humans Idioma: En Revista: Liver Int Assunto da revista: GASTROENTEROLOGIA Ano de publicação: 2021 Tipo de documento: Article País de afiliação: França