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Further characterization of clinical and laboratory features in VEXAS syndrome: large-scale analysis of a multicentre case series of 116 French patients.
Georgin-Lavialle, S; Terrier, B; Guedon, A F; Heiblig, M; Comont, T; Lazaro, E; Lacombe, V; Terriou, L; Ardois, S; Bouaziz, J-D; Mathian, A; Le Guenno, G; Aouba, A; Outh, R; Meyer, A; Roux-Sauvat, M; Ebbo, M; Zhao, L P; Bigot, A; Jamilloux, Y; Guillotin, V; Flamarion, E; Henneton, P; Vial, G; Jachiet, V; Rossignol, J; Vinzio, S; Weitten, T; Vinit, J; Deligny, C; Humbert, S; Samson, M; Magy-Bertrand, N; Moulinet, T; Bourguiba, R; Hanslik, T; Bachmeyer, C; Sebert, M; Kostine, M; Bienvenu, B; Biscay, P; Liozon, E; Sailler, L; Chasset, F; Audemard-Verger, A; Duroyon, E; Sarrabay, G; Borlot, F; Dieval, C; Cluzeau, T.
Afiliação
  • Georgin-Lavialle S; Sorbonne Université, AP-HP, Hôpital Tenon, Service de Médecine Interne, CeRéMAIA, Paris, France.
  • Terrier B; Department of Internal Medicine, University of Paris, AP-HP, Cochin Hospital, Paris, France.
  • Guedon AF; Sorbonne Université, Inserm, Institut Pierre-Louis d'Epidémiologie et de Santé Publique, Département de Santé Publique, Hôpital Saint-Antoine, AP-HP, Paris, France.
  • Heiblig M; Department of Haematology, University Hospital of Lyon, Hospices Civils de Lyon, Lyon, France.
  • Comont T; Department of Internal Medicine and Clinical Immunology, University Hospital of Toulouse, Toulouse, France.
  • Lazaro E; Department of Internal Medicine and Infectious Diseases, Hôpital Haut-Lévêque, Bordeaux, France.
  • Lacombe V; Department of Internal Medicine, Angers University Hospital, Angers, France.
  • Terriou L; Department of Internal Medicine, Lille University Hospital, Lille, France.
  • Ardois S; Service de Médecine Interne, CHU de Rennes, Rennes, France.
  • Bouaziz JD; Université de Paris, Service de Dermatologie, Hôpital Saint Louis, AP-HP, INSERM U944, Paris, France.
  • Mathian A; Assistance Publique-Hôpitaux de Paris, Groupement Hospitalier Pitié-Salpêtrière, French National Referral Center for Systemic Lupus Erythematosus, Antiphospholipid Antibody Syndrome and Other Autoimmune Disorders, Service de Médecine Interne 2, Institut E3M, Paris, France.
  • Le Guenno G; Department of Internal Medicine and Clinical Immunology, University Hospital Centre of Bordeaux, Saint Andre Hospital, Bordeaux, France.
  • Aouba A; CHU de Clermont-Ferrand, Hôpital Estaing, Service de Médecine Interne, Clermont-Ferrand, France.
  • Outh R; Department of Internal Medicine, Caen Université, Hôpital de Caen, Caen, France.
  • Meyer A; Service de Médecine Interne et Générale, Centre Hospitalier de Perpignan, Perpignan, France.
  • Roux-Sauvat M; Service d'Immunologie Clinique et Médecine Interne, Nouvel Hôpital Civil, CHU Strasbourg, Strasbourg, France.
  • Ebbo M; GHND, Centre Hospitalier Pierre Oudot, BP 40348, Bourgoin-Jallieu Cedex, France.
  • Zhao LP; Department of Internal Medicine, Aix Marseille Université, AP-HM, Hôpital de la Timone, Marseille, France.
  • Bigot A; Hematology Department, AP-HP, CHU of Saint Louis, Paris, France.
  • Jamilloux Y; Department of Internal and Clinical Medicine, University of Tours, Tours, France.
  • Guillotin V; Department of Internal Medicine and Clinical Immunology, University Hospital of Lyon, Hospices Civils de Lyon, Lyon, France.
  • Flamarion E; Department of Internal Medicine and Clinical Immunology, University Hospital Centre of Bordeaux, Saint Andre Hospital, Bordeaux, France.
  • Henneton P; CHU de Clermont-Ferrand, Hôpital Estaing, Service de Médecine Interne, Clermont-Ferrand, France.
  • Vial G; Université de Paris, Service de Médecine Interne, Paris, France.
  • Jachiet V; Service de Médecine Vasculaire, CHU Montpellier, Montpellier, France.
  • Rossignol J; Department of Internal Medicine and Clinical Immunology, University Hospital Centre of Bordeaux, Saint Andre Hospital, Bordeaux, France.
  • Vinzio S; CHU de Clermont-Ferrand, Hôpital Estaing, Service de Médecine Interne, Clermont-Ferrand, France.
  • Weitten T; Sorbonne Université, AP-HP, Hôpital Saint Antoine, Service de Médecine Interne et Inflammation-Immunopathology-Biotherapy Department (DMU i3), Paris, France.
  • Vinit J; Université de Paris, Service d'Hématologie, Necker Enfants Malades, Paris, France.
  • Deligny C; Service de Médecine Interne, Groupe Hospitalier Mutualiste, Grenoble, France.
  • Humbert S; Service de Médecine Interne, Centre Hospitalier (CHICAS), Gap, France.
  • Samson M; Service de Médecine Interne, Centre Hospitalier, Chalons, France.
  • Magy-Bertrand N; Service de Rhumatologie - Médecine Interne 5D, CHU de Martinique, Hôpital P. Zobda-Quitman, France.
  • Moulinet T; CHU de Besançon, Service de Médecine Interne, Besançon, France.
  • Bourguiba R; Department of Internal Medicine and Clinical Immunology, Dijon University Hospital, Dijon, France.
  • Hanslik T; CHU de Besançon, Service de Médecine Interne, Besançon, France.
  • Bachmeyer C; Department of Internal Medicine and Clinical Immunology, Regional Competence Center for Systemic and Autoimmune Rare Diseases, Nancy University Hospital, UMR 7365, IMoPA, Lorraine University, CNRS, Vandoeuvre-lès-Nancy, France.
  • Sebert M; Sorbonne Université, AP-HP, Hôpital Tenon, Service de Médecine Interne, CeRéMAIA, Paris, France.
  • Kostine M; AP-HP, Hôpital Ambroise Paris, Service de Médecine Interne, Paris, France.
  • Bienvenu B; Sorbonne Université, AP-HP, Hôpital Tenon, Service de Médecine Interne, CeRéMAIA, Paris, France.
  • Biscay P; Hematology Department, AP-HP, CHU of Saint Louis, Paris, France.
  • Liozon E; Department of Rheumatology, Hôpital Haut-Lévesque, Bordeaux, France.
  • Sailler L; Hôpital Saint Joseph, Service de Médecine Interne, Marseille, France.
  • Chasset F; Clinique Mutualiste Pessac Médecine Interne, Pessac, France.
  • Audemard-Verger A; Service de Médecine Interne, CHU Dupuytren, Limoges, France.
  • Duroyon E; Department of Internal Medicine, University Hospital of Toulouse, Toulouse, France.
  • Sarrabay G; Sorbonne Université, Hôpital Tenon, Service de Dermatologie et Allergologie et Inflammation-Immunopathology-Biotherapy Department (DMU i3), Paris, France.
  • Borlot F; Department of Internal and Clinical Medicine, University of Tours, Tours, France.
  • Dieval C; Service d'Hématologie Biologique, DMU BioPhyGen GH AP-HP, Centre-University de Paris, Paris, France.
  • Cluzeau T; Laboratory of Rare and Autoinflammatory Genetic Diseases and Reference Centre for Autoinflammatory Diseases and Amyloidosis (CEREMAIA), CHU Montpellier, University of Montpellier, Montpellier, France.
Br J Dermatol ; 186(3): 564-574, 2022 03.
Article em En | MEDLINE | ID: mdl-34632574

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Síndromes Mielodisplásicas / Gamopatia Monoclonal de Significância Indeterminada Tipo de estudo: Clinical_trials / Diagnostic_studies / Prognostic_studies Limite: Humans Idioma: En Revista: Br J Dermatol Ano de publicação: 2022 Tipo de documento: Article País de afiliação: França

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Síndromes Mielodisplásicas / Gamopatia Monoclonal de Significância Indeterminada Tipo de estudo: Clinical_trials / Diagnostic_studies / Prognostic_studies Limite: Humans Idioma: En Revista: Br J Dermatol Ano de publicação: 2022 Tipo de documento: Article País de afiliação: França