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Propionic acidemia in mice: Liver acyl-CoA levels and clinical course.
Zhao, Chen; Wang, Youlin; Yang, Hao; Wang, Shupei; Tang, Marie-Christine; Cyr, Denis; Parente, Fabienne; Allard, Pierre; Waters, Paula; Furtos, Alexandra; Yang, Gongshe; Mitchell, Grant A.
Afiliação
  • Zhao C; Key Laboratory of Animal Genetics, Breeding and Reproduction of Shaanxi Province, Laboratory of Animal Fat Deposition and Muscle Development, College of Animal Science and Technology, Northwest A & F University, Yangling, Shaanxi, China; Medical Genetics Service, Department of Pediatrics and Res
  • Wang Y; Medical Genetics Service, Department of Pediatrics and Research Center, CHU Sainte-Justine and Université de Montréal, Montreal, Quebec, Canada.
  • Yang H; Medical Genetics Service, Department of Pediatrics and Research Center, CHU Sainte-Justine and Université de Montréal, Montreal, Quebec, Canada.
  • Wang S; Medical Genetics Service, Department of Pediatrics and Research Center, CHU Sainte-Justine and Université de Montréal, Montreal, Quebec, Canada.
  • Tang MC; Département de Chimie, Université de Montréal, Montreal, Quebec, Canada.
  • Cyr D; Medical Genetics Service, Department of Laboratory Medicine, CHU Sherbrooke and Department of Pediatrics, Université de Sherbrooke, Quebec, Canada.
  • Parente F; Biochemical Genetics Laboratory, CHU Sainte-Justine, Montreal, Quebec, Canada.
  • Allard P; Biochemical Genetics Laboratory, CHU Sainte-Justine, Montreal, Quebec, Canada.
  • Waters P; Medical Genetics Service, Department of Laboratory Medicine, CHU Sherbrooke and Department of Pediatrics, Université de Sherbrooke, Quebec, Canada.
  • Furtos A; Département de Chimie, Université de Montréal, Montreal, Quebec, Canada.
  • Yang G; Key Laboratory of Animal Genetics, Breeding and Reproduction of Shaanxi Province, Laboratory of Animal Fat Deposition and Muscle Development, College of Animal Science and Technology, Northwest A & F University, Yangling, Shaanxi, China. Electronic address: gsyang999@hotmail.com.
  • Mitchell GA; Medical Genetics Service, Department of Pediatrics and Research Center, CHU Sainte-Justine and Université de Montréal, Montreal, Quebec, Canada. Electronic address: grant.mitchell.med@ssss.gouv.qc.ca.
Mol Genet Metab ; 135(1): 47-55, 2022 01.
Article em En | MEDLINE | ID: mdl-34896004

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Hiperamonemia / Acidemia Propiônica Tipo de estudo: Prognostic_studies Limite: Animals / Female / Humans / Male Idioma: En Revista: Mol Genet Metab Assunto da revista: BIOLOGIA MOLECULAR / BIOQUIMICA / METABOLISMO Ano de publicação: 2022 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Hiperamonemia / Acidemia Propiônica Tipo de estudo: Prognostic_studies Limite: Animals / Female / Humans / Male Idioma: En Revista: Mol Genet Metab Assunto da revista: BIOLOGIA MOLECULAR / BIOQUIMICA / METABOLISMO Ano de publicação: 2022 Tipo de documento: Article