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A large dedifferentiated retroperitoneal liposarcoma extended to the testis: a rare case report.
Habonimana, Patrice; Niyonkuru, Evrard; Nisabwe, Simon; Mazti, Asmae; Moataz, Amine; Dakir, Mohamed; Debbagh, Adil; Aboutaieb, Rachid.
Afiliação
  • Habonimana P; Urology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
  • Niyonkuru E; Pathology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
  • Nisabwe S; Pathology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
  • Mazti A; Pathology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
  • Moataz A; Urology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
  • Dakir M; Urology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
  • Debbagh A; Urology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
  • Aboutaieb R; Urology Department, Ibn Rochd University Hospital Center, Casablanca, Morocco.
J Surg Case Rep ; 2023(5): rjad162, 2023 May.
Article em En | MEDLINE | ID: mdl-37255958
ABSTRACT
Liposarcomas are neoplasms of mesodermal origin representing less than 1% of all malignant tumors and 1 to 2% of urogenital lesions. Primary retroperitoneal liposarcomas extending into the inguinal canal are rare. We present the case of a large retroperitoneal liposarcoma invading the left testicle and its spermatic cord. It was diagnosed by imaging as a large mass that compresses surrounding abdominal structures and communicating with the inguinal canal. A surgical intervention consisting of en bloc resection of the tumor and the left testicle with its cord was performed by 2 routes, intercostal and inguinal. Histology showed a dedifferentiated liposarcoma, which is a rare entity with a high rate of malignancy and a poor prognosis. The treatment of choice is wide surgical resection with clear margins; chemotherapy and radiotherapy are less sensitive. The patient did not manifest any particular complaints during the first six months after surgery.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Tipo de estudo: Prognostic_studies Idioma: En Revista: J Surg Case Rep Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Marrocos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Tipo de estudo: Prognostic_studies Idioma: En Revista: J Surg Case Rep Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Marrocos