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Muir-Torre syndrome associated with a family history of hyperlipidemia.
Ródenas, J M; Herranz, M T; Tercedor, J; López, B; Naranjo, R; Delgado, V.
Afiliação
  • Ródenas JM; Department of Dermatology, Hospital Universitario, Granada, Spain.
J Am Acad Dermatol ; 28(2 Pt 2): 285-8, 1993 Feb.
Article em En | MEDLINE | ID: mdl-8436639
ABSTRACT
The Muir-Torre syndrome is a rare disorder characterized by sebaceous neoplasms of the skin and multiple visceral malignancies. The syndrome appears to be a familial, autosomal dominant condition. We diagnosed this syndrome in a previously unreported patient and found a personal and family history of malignancies and hyperlipidemia. The association of Muir-Torre syndrome with a family history of hyperlipidemia, another autosomal dominant condition, has not been previously reported. The possible genetic relationship between the two disorders is discussed.
Assuntos
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Neoplasias das Glândulas Sebáceas / Síndromes Neoplásicas Hereditárias / Hiperlipidemia Familiar Combinada / Neoplasias Intestinais Tipo de estudo: Risk_factors_studies Limite: Aged / Humans / Male Idioma: En Revista: J Am Acad Dermatol Ano de publicação: 1993 Tipo de documento: Article País de afiliação: Espanha
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Neoplasias das Glândulas Sebáceas / Síndromes Neoplásicas Hereditárias / Hiperlipidemia Familiar Combinada / Neoplasias Intestinais Tipo de estudo: Risk_factors_studies Limite: Aged / Humans / Male Idioma: En Revista: J Am Acad Dermatol Ano de publicação: 1993 Tipo de documento: Article País de afiliação: Espanha