Telemedicine in Cleft Care: Reliability and Predictability in Regional and International Practice Settings.

BACKGROUND: Regional and international cleft care providers are challenged in their ability to deliver reliable, comprehensive care. Our institution utilizes video teleconferencing to facilitate initial evaluation and postoperative cleft care. This study describes our experience using telemedicine, generates a perioperative treatment algorithm using this technology, and compares cost-utility of telemedicine to in-person ambulatory visits when regional practices are involved. METHODS: A 5-year retrospective review of all cleft patients evaluated in an ambulatory setting was conducted. Patient demographics and location, number, and type of telemedicine visits were recorded. Specific treatment algorithms utilizing telemedicine for perioperative care for primary and secondary cleft lip and nasal repair, palatoplasty, and operation for velopharyngeal insufficiency are described. A cost-utility analysis was performed comparing distances between patient homes and primary hub versus telemedicine clinic sites. RESULTS: Five hundred nineteen patients were identified; 18.1% attended at least 1 teleconferencing visit. Postoperative follow-up was 100%. The majority of screening, preoperative, and postoperative care was provided using telemedicine. In-person evaluations were performed when intraoral assessments were necessary. Telemedicine visits were associated with an average savings of 239 miles per visit in the United States and 578 miles per visit in Mexico. CONCLUSIONS: Video teleconferencing can be used to provide comprehensive regional and international cleft care to facilitate initial evaluations and consistent follow-up. This technology can alleviate the travel burden on families and cleft care providers practicing over a large geographic radius.

Bone mineral density and functional measures in patients with arthrogryposis.

BACKGROUND: Patients with arthrogryposis often report decreased ambulation and physical activity. Given that skeletal mineralisation is responsive to force, we identified the need to characterize bone mineral density and functional measures in this population, and conducted a cross-sectional study to establish a reference for future investigations. METHODS: Thirty consecutive patients aged 5 to 18 years with either the diagnosis of amyoplasia or nonsyndromic arthrogryposis with predominantly lower extremity involvement underwent bone densitometry testing, and lumbar spine Z-scores were calculated against an age and sex-matched control population as is customary in children. Pediatric outcomes data collection instrument (PODCI) and functional independence measure for Children (WeeFIM) assessment forms were completed. Mean Z-scores, PODCI, and WeeFIM scores were calculated. Statistical analysis was performed to compare lumbar spine Z-scores between patients divided by ambulatory status and to correlate WeeFIM and PODCI scores. RESULTS: Mean lumbar spine Z-score was -0.47, with 73% of Z-scores being <0. Mean Z-score among nonambulators or home ambulators was -1.05, as compared to a mean Z-score among limited and unlimited community ambulators of -0.14 with a trend toward significance (P=0.10), and a dose-response relationship between higher bone density and increasing ambulatory function. Mean WeeFIM self-care and mobility quotient scores were 67.5/100 and 70.9/100, respectively. PODCI normative scores were decreased for upper extremity (10/50), transfer/basic mobility (-17/50), and sports/physical function (4/50), but normal in pain/comfort (45/50) and happiness (49/50). A linear relationship was noted between functional ambulation level and WeeFIM quotient and PODCI normative scores. There was good correlation between WeeFIM mobility and PODCI transfers and basic mobility standardised scores (R=0.86). CONCLUSIONS: This is the first study to measure bone mineral density in children with arthrogryposis, and shows it to be lower than age-matched means, especially in patients with limited ambulation. Objective measures of functional ability (WeeFIM and PODCI) are decreased and demonstrate a linear relationship with ambulatory level. Further investigation is needed to quantify long-term effects of entering adulthood with below average bone mineral density in patients with arthrogryposis. LEVEL OF EVIDENCE: Level II.

Corrective osteotomies and osteosynthesis for supination contracture of the forearm in children.

PURPOSE: The purpose of this study was to present the authors' experience with corrective osteotomies of the forearm for supination contracture in children. METHODS: Fourteen patients with supination contracture of the forearm due to brachial plexus lesion (11), poliomyelitis residuals (2), or Monteggia fracture malunion (1) underwent distal ulnar osteotomy without fixation and subsequent midradial osteotomy with plate fixation to produce a position of greater pronation. A minimum of 6 months' follow-up was required to be included in the series. RESULTS: Ten boys and 4 girls whose mean age was 11 years underwent surgery between 1998 and 2006 to correct a supination contracture. The mean preoperative contracture measured 80 degrees of supination. The final mean postoperative correction was 104 degrees, whereas the final mean position of pronation was 24 degrees. CONCLUSIONS: Distal ulnar and midradial osteotomies are effective in the treatment of supination deformities of the forearm with little risk of complication or need for additional surgery. Radial fixation is important, but ulnar fixation is not required. Both osteotomies must be complete before plate fixation of the radius to realize maximal correction. LEVEL OF EVIDENCE: Level IV.