[Refractory, incomplete and atypical Kawasaki disease. Case report and review of the literature]. / Enfermedad de Kawasaki refractaria, incompleta y atípica. Informe de un caso y revisión de la bibliografía.

We report the case of a 2 year 7 month old boy with the diagnosis of incomplete and atypical Kawasaki disease, whom showed only two of the classical criteria: fever and conjunctival injection without exudate, presenting clinical manifestations that are reported less often, such as gallbladder hydrops, aseptic meningitis, arthralgia, sterile pyuria, coronary aneurysms and myocardial ischemia. This patient had recurrent and refractory Kawasaki disease not responding to treatment with intravenous immunoglobulin and thus requiring steroids and immunosuppressive management.