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Diffuse pulmonary arteriovenous malformations in a teenager with corrected total anomalous pulmonary venous drainage.
Pfleger, Andreas; Gamillscheg, Andreas; Popper, Helmut H; Smolle-Jüttner, Freyja-Maria; Zach, Maximilian S.
Afiliación
  • Pfleger A; Respiratory and Allergic Disease Division, Pediatric Department, University of Graz, Graz, Austria. andreas.pfleger@meduni-graz.at
Respiration ; 74(1): 106-9, 2007.
Article en En | MEDLINE | ID: mdl-16106112
ABSTRACT
UNLABELLED This case report describes a 13-year-old boy with diffuse microvascular pulmonary arteriovenous malformations, in whom total anomalous pulmonary venous drainage had been corrected surgically in the newborn period. Contrast transesophageal echocardiography, cardiac catheterization and a lung perfusion scan suggested, and lung biopsy confirmed the diagnosis in our patient. Treatment with nifedipin was commenced.

CONCLUSION:

This case illustrates the diagnostic difficulties with this rare malformation.
Asunto(s)
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Banco de datos: MEDLINE Asunto principal: Malformaciones Arteriovenosas / Arteria Pulmonar / Venas Pulmonares / Telangiectasia Hemorrágica Hereditaria Tipo de estudio: Diagnostic_studies Límite: Adolescent / Humans / Male Idioma: En Revista: Respiration Año: 2007 Tipo del documento: Article País de afiliación: Austria
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Banco de datos: MEDLINE Asunto principal: Malformaciones Arteriovenosas / Arteria Pulmonar / Venas Pulmonares / Telangiectasia Hemorrágica Hereditaria Tipo de estudio: Diagnostic_studies Límite: Adolescent / Humans / Male Idioma: En Revista: Respiration Año: 2007 Tipo del documento: Article País de afiliación: Austria