Blue rubber bleb naevus syndrome and Chiari malformation: high risk of peroperative haemorrhage.
Turk Neurosurg
; 23(6): 818-20, 2013.
Article
en En
| MEDLINE
| ID: mdl-24310471
ABSTRACT
Blue rubber bleb naevus syndrome is an uncommon disorder whereby patients possess cutaneous vascular malformations. Cranial malformations have been rarely reported in the literature. We report the first ever case of a patient with blue rubber bleb naevus syndrome (BRBNS), who was found to have a symptomatic Chiari malformation and prominent subcutaneous vascular malformations in communication with the intracranial venous sinuses. In our case, a routine operation for Chiari malformation was complicated by significant blood loss. The operative hazards are presented along with suggested peri-operative management strategies when carrying out neurosurgical operations on patients with BRBNS. A brief literature review is included.
Texto completo:
1
Banco de datos:
MEDLINE
Asunto principal:
Malformación de Arnold-Chiari
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Neoplasias Cutáneas
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Nevo Azul
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Hemorragia Posoperatoria
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Procedimientos Neuroquirúrgicos
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Hemorragias Intracraneales
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Neoplasias Gastrointestinales
/
Complicaciones Intraoperatorias
Tipo de estudio:
Etiology_studies
/
Risk_factors_studies
Límite:
Adolescent
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Female
/
Humans
Idioma:
En
Revista:
Turk Neurosurg
Asunto de la revista:
NEUROCIRURGIA
Año:
2013
Tipo del documento:
Article
País de afiliación:
Reino Unido