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The CARD11-BCL10-MALT1 (CBM) signalosome complex: Stepping into the limelight of human primary immunodeficiency.
Turvey, Stuart E; Durandy, Anne; Fischer, Alain; Fung, Shan-Yu; Geha, Raif S; Gewies, Andreas; Giese, Thomas; Greil, Johann; Keller, Bärbel; McKinnon, Margaret L; Neven, Bénédicte; Rozmus, Jacob; Ruland, Jürgen; Snow, Andrew L; Stepensky, Polina; Warnatz, Klaus.
Afiliación
  • Turvey SE; Department of Pediatrics, Child & Family Research Institute, and BC Children's Hospital, University of British Columbia, Vancouver, British Columbia, Canada. Electronic address: sturvey@cw.bc.ca.
  • Durandy A; National Institute of Health and Medical Research and the Department of Immunology and Hematology, Assistance Publique-Hopitaux de Paris, Necker Children's Hospital, Paris, and Descartes-Sorbonne Paris Cité University of Paris, Imagine Institute, Paris, France.
  • Fischer A; National Institute of Health and Medical Research and the Department of Immunology and Hematology, Assistance Publique-Hopitaux de Paris, Necker Children's Hospital, Paris, and Descartes-Sorbonne Paris Cité University of Paris, Imagine Institute, Paris, France; Unité d'immuno-hématologie pédiatrique
  • Fung SY; Department of Pediatrics, Child & Family Research Institute, and BC Children's Hospital, University of British Columbia, Vancouver, British Columbia, Canada.
  • Geha RS; Division of Immunology, Boston Children's Hospital and Department of Pediatrics, Harvard Medical School, Boston, Mass.
  • Gewies A; German Cancer Consortium (DKTK), partner site Munich at the Institut für Klinische Chemie und Pathobiochemie, Klinikum rechts der Isar, Technische Universität München, Munich, and German Cancer Research Center (DKFZ), Heidelberg, Germany.
  • Giese T; Institute for Immunology, University of Heidelberg, Heidelberg, Germany.
  • Greil J; Department of Pediatric Oncology, Hematology and Immunology, University of Heidelberg, Heidelberg, Germany.
  • Keller B; Centre for Chronic Immunodeficiency (CCI), University Medical Center Freiburg and University of Freiburg, Freiburg, Germany.
  • McKinnon ML; Department of Medical Genetics, Child & Family Research Institute and BC Children's Hospital, University of British Columbia, Vancouver, British Columbia, Canada.
  • Neven B; Unité d'immuno-hématologie pédiatrique, Hôpital Necker-Enfant Malades, Assistance Publique des Hôpitaux de Paris (APHP), Paris, France.
  • Rozmus J; Department of Pediatrics, Child & Family Research Institute, and BC Children's Hospital, University of British Columbia, Vancouver, British Columbia, Canada.
  • Ruland J; Institut für Klinische Chemie und Pathobiochemie, Klinikum rechts der Isar, Technische Universität München, Munich, Germany.
  • Snow AL; Department of Pharmacology, Uniformed Services University of the Health Sciences, Bethesda, Md.
  • Stepensky P; Pediatric Hematology-Oncology and Bone Marrow Transplantation, Hadassah Hebrew University Medical Center, Jerusalem, Israel.
  • Warnatz K; Centre for Chronic Immunodeficiency (CCI), University Medical Center Freiburg and University of Freiburg, Freiburg, Germany.
J Allergy Clin Immunol ; 134(2): 276-84, 2014 Aug.
Article en En | MEDLINE | ID: mdl-25087226

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Linfocitos B / Caspasas / Proteínas Adaptadoras Transductoras de Señales / Proteínas Adaptadoras de Señalización CARD / Guanilato Ciclasa / Síndromes de Inmunodeficiencia / Proteínas de Neoplasias Tipo de estudio: Diagnostic_studies Límite: Humans Idioma: En Revista: J Allergy Clin Immunol Año: 2014 Tipo del documento: Article

Texto completo: 1 Banco de datos: MEDLINE Asunto principal: Linfocitos B / Caspasas / Proteínas Adaptadoras Transductoras de Señales / Proteínas Adaptadoras de Señalización CARD / Guanilato Ciclasa / Síndromes de Inmunodeficiencia / Proteínas de Neoplasias Tipo de estudio: Diagnostic_studies Límite: Humans Idioma: En Revista: J Allergy Clin Immunol Año: 2014 Tipo del documento: Article