A case of acute liver failure caused by Budd-Chiari syndrome salvaged by brain-dead donor liver transplantation.
Clin J Gastroenterol
; 17(1): 84-92, 2024 Feb.
Article
en En
| MEDLINE
| ID: mdl-37773425
ABSTRACT
A 24-year-old man was admitted to our hospital with abdominal distension. He was found to have acute liver failure and diagnosed with Budd-Chiari syndrome based on angiography and liver biopsy. Liver transplantation was deemed necessary when angiography showed extensive thrombotic occlusion of the hepatic veins and liver biopsy revealed submassive hepatic necrosis. The patient was found to have the JAK2V617F mutation, indicating a myeloproliferative neoplasm as the background disease. He developed hepatic encephalopathy but remained conscious on on-line hemodiafiltration. Brain-dead donor liver transplantation was performed on hospital day 30. Since then, the patient has remained well.
Palabras clave
Texto completo:
1
Banco de datos:
MEDLINE
Asunto principal:
Trasplante de Hígado
/
Fallo Hepático Agudo
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Síndrome de Budd-Chiari
Límite:
Adult
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Humans
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Male
Idioma:
En
Revista:
Clin J Gastroenterol
Año:
2024
Tipo del documento:
Article
País de afiliación:
Japón