Sudden bilateral sensorineural hearing loss associated with urticarial vasculitis.

BACKGROUND: Bilateral sensorineural hearing loss associated with recurrent urticarial skin lesions may be signs of underlying Muckle-Wells syndrome. Previous reports have described the hearing loss to be progressive in nature. METHOD: To our knowledge, this paper presents the first published case of sudden onset, bilateral sensorineural hearing loss associated with urticarial vasculitis due to underlying Muckle-Wells syndrome. RESULTS: The patient underwent a cochlear implantation with a modest outcome. CONCLUSION: Cochlear implantation may help to rehabilitate sudden hearing loss associated with this condition, but early diagnosis may allow treatment with interleukin-1ß inhibitors such as anakinra.

Electric acoustic stimulation of the auditory system: experience and results of ten patients using MED-EL's M and FlexEAS electrodes.

OBJECTIVE: To evaluate the hearing preservation rate and speech perception scores in patients with profound high frequency hearing loss and acoustically aidable low frequency hearing, managed with the MED-EL electric acoustic stimulation system referenced to the insertion depth of the electrode array. STUDY DESIGN: Retrospective data analysis. PARTICIPANTS AND SETTING: Ten patients implanted at the Auditory Implant Centre, Guy's and St Thomas's Hospital, London, UK. MAIN OUTCOME MEASURES: Pure tone audiometry, speech perception tests and electrode insertion depth angle. RESULTS: Postoperatively, functional hearing preservation allowing electric acoustic stimulation was achieved in eight patients and total preservation of residual hearing in five patients with follow-up periods of more than 12 months. Three of four (75%) patients with an insertion depth of >360 degrees had a threshold shift of >25 dB, and all four patients had a threshold shift of >10 dB. All patients with total hearing preservation had the electrode inserted up to 360 degrees at maximum. Overall, speech perception outcomes increased significantly and hearing impairment was significantly reduced after electric acoustic stimulation or electric stimulation alone as compared with the preoperative scores. CONCLUSION: Electric acoustic stimulation provides significant benefit to individuals with profound high frequency hearing loss. Studies with larger number of patients are needed to establish the optimal electrode insertion angle as well as to further analyse the benefit of electric acoustic stimulation.

CT and MR imaging cochlear distance measurements may predict cochlear implant length required for a 360 degrees insertion.

BACKGROUND AND PURPOSE: A preoperative prediction of the 360 degrees point insertion depth would aid the planning of electric acoustic stimulation (EAS) implantation. The purpose of this study was to establish whether the distance between the round window and the opposite cochlear wall on CT or MR imaging may be used to predict the length of a cochlear implant electrode array required to be inserted to the 360 degrees point of the basal turn. MATERIALS AND METHODS: CT and MR imaging data were studied in 19 patients undergoing cochlear implantation. Distances were measured between the round window and the opposite outer cochlear wall on an oblique paracoronal reformatted image. Adjusted distance measurements were applied to a spiral function to estimate the length of an electrode array extending between the round window entry point and the 360 degrees point. This was compared with measurements of implant length to this insertion depth on postoperative CT. RESULTS: Intraobserver reproducibility for each of the 2 observers was r = 0.85/0.55 for CT and r = 0.87/0.67 for MR imaging. Interobserver reproducibility was r = 0.68 for CT and r = 0.84 for MR imaging. There was no bias between CT and MR imaging measurements, with a mean difference of less than 0.1 mm. CT and MR imaging estimates markedly correlated with the actual length of the electrode array extending to the 360 degrees insertion depth (SD between the estimated and actual length was 0.84 mm for CT and 0.87 mm for MR imaging). CONCLUSIONS: CT and MR imaging measures of cochlear distance (CD) were used to predict insertion depths to 360 degrees , and these were markedly concordant with the actual length of the electrode array required to reach this point. MR imaging measurements were more precise and similar in accuracy to those obtained with CT.

Non-sutured fixation of cochlear implants using a minimally-invasive approach.

The minimal invasive techniques have become the main stay of the surgical approach for the cochlear implant. Securing the implant with sutures can be challenging due to the limited access and awkward operating angle. We have developed a non-sutured technique to secure the implant by placing and securing the proximal end of the electrode into a bony groove. Our series supports the notion that the technique is suitable for implant cases in which the patient's age is older than 18 months.

Submucous resection of the nasal septum as an outpatient procedure.

We report our experience of submucous resection of the nasal septum under local anaesthesia as an outpatient procedure. We have audited 50 consecutive cases and compared the results with a similar group of patients in whom the operation was carried out in the usual way under general anaesthesia. We have found the procedure to be safe, effective and economically advantageous.