RESUMO
Inflammatory myofibroblastic tumour (IMT) is a rare mesenchymal tumour. It is usually benign but may behave as a malignant tumour with multiple recurrences and metastases. We present the case of a young woman with weight loss associated with diffuse abdominal pain, who was shown to have a large pancreatic mass. Investigation revealed fusocellular mesenchymal neoplasia, compatible with the diagnosis of IMT. As the mass was unresectable, glucocorticoid therapy was initiated with an excellent response and regression of the tumour. LEARNING POINTS: Inflammatory myofibroblastic tumour (IMT) is a rare entity.Since IMT can occur in different locations, its clinical presentation is varied, with non-specific symptoms.Prognosis is usually benign, but relapse and metastasis have been reported.