1.
Neuromuscul Disord
; 36: 38-41, 2024 Mar.
Artigo
em Inglês
| MEDLINE
| ID: mdl-38350265
RESUMO
Contracturing granulomatous myositis is a rare myopathy in which patients present with flexion contractures of the upper limbs in addition to slowly progressive muscle weakness and pain. Whether it represents a distinct nosological entity remains a point of discussion. We present a patient with isolated granulomatous disease of the muscle that responded very well to intravenous immunoglobulins after treatment failure of corticosteroids and methotrexate.