Congenital hemangiopericytoma presenting as rectal bleeding in a neonate: a case report.

Hemangiopericytoma is a rare soft tissue lesion originating from capillary pericytes that can occur anywhere vascular capillaries are found. It is an uncommon tumor found typically in adults but rarely in children. We describe a previously unreported case of an intraluminal lesion in a neonate.

Congenital fibrolipoma of anal canal.

Although rare, congenital lipomatosis presents during first few months of life as large sub-cutaneous fatty masses on chest with extension into skeletal muscle bundles. Only a few such cases have been reported in the literature. A rare case of congenital fibrolipoma of anal canal in a 3-day-old male child is being documented in the present report.

The management of retrorectal congenital tumors.

Although retrorectal congenital tumors are still rare, the number of the observed ones is destined to increase, as methods by imaging become routinely used in the clinical practice. By presenting three clinical cases the authors describe the surgical technique of the anterior route they performed for the management of such formations. The abdominal approach had no postoperative complications, short hospital stay, no neurological consequences and good long-term results. There has been no evidence of recurrence thus far. Once diagnosed, the removal of retrorectal lesions should be mandatory. A precise definition of the extent of the tumors and of their relationships with the surrounding tissue and organs is necessary to perform maneuvers of total excision. For this reason an abdominal approach is recommended.

Congenital anorectal teratoma: report of a case.

This is the first reported case of congenital anorectal teratoma. Total disconnection from the coccyx and mucomembranous covering distinguish this tumor from the more common sacrococcygeal teratoma. Complete surgical excision is important to avoid recurrence or malignant transformation.

Retrorectal cyst-hamartomas: CT diagnosis.

Retrorectal cyst-hamartomas (RRCH) are congenital lesions characterized by the presence of cysts lined by multiple types of epithelium, often predominantly mucin-secreting. Three cases of RRCH are presented with their associated histologic and CT findings. The lesion requires complete surgical excision to prevent complications of recurrence, infection, or metastasis.

An unusual hamartomatous malformation of the rectosigmoid presenting as an irreducible rectal prolapse and necessitating rectosigmoid resection in a 14-week-old infant.

A 14-week-old female infant presented with an irreducible rectal prolapse and a large polypoid tumor at the tip of the prolapsed mucosa. The tumor and prolapsed rectum were resected. Four weeks after the operation, profuse rectal bleeding occurred and a second similar tumor was diagnosed by endoscopy in the sigmoid colon. Laparotomy, rectosigmoid resection, and endorectal pull-through were performed. At operation, the serosal surface showed ragged polypoid lesions and an abnormal angiomatous vascularization. The postoperative course was uneventful. The histology suggested a congenital mucosal malformation. This pathology is unique in our experience and we have been unable to find anything resembling it in the literature. At age two years a Sertoli cell tumor developed in the girl with pubertas precox and a recurrent colonic polyp of the Peutz-Jeghers type.