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Frataxin silencing inactivates mitochondrial Complex I in NSC34 motoneuronal cells and alters glutathione homeostasis.
Carletti, Barbara; Piermarini, Emanuela; Tozzi, Giulia; Travaglini, Lorena; Torraco, Alessandra; Pastore, Anna; Sparaco, Marco; Petrillo, Sara; Carrozzo, Rosalba; Bertini, Enrico; Piemonte, Fiorella.
Afiliación
  • Carletti B; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. carletti.barbara@tiscali.it.
  • Piermarini E; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. emanuela.piermarini@opbg.net.
  • Tozzi G; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. giulia.tozzi@opbg.net.
  • Travaglini L; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. lorena.travaglini@opbg.net.
  • Torraco A; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. alessandra.torraco@opbg.net.
  • Pastore A; Biochemistry Laboratory, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. anna.pastore@opbg.net.
  • Sparaco M; Division of Neurology, Department of Neurosciences, Azienda Ospedaliera, "G. Rummo", Via Pacevecchia 53, 82100 Benevento, Italy. marcosparaco@alice.it.
  • Petrillo S; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. sara.petrillo@opbg.net.
  • Carrozzo R; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. rosalba.carrozzo@opbg.net.
  • Bertini E; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. enricosilvio.bertini@opbg.net.
  • Piemonte F; Unit for Neuromuscular and Neurodegenerative Diseases, Children's Hospital and Research Institute "Bambino Gesù", Piazza S. Onofrio 4, 00165 Rome, Italy. fiorella.piemonte@opbg.net.
Int J Mol Sci ; 15(4): 5789-806, 2014 Apr 04.
Article en En | MEDLINE | ID: mdl-24714088

Texto completo: 1 Colección: 01-internacional Asunto principal: Proteínas de Unión a Hierro / Complejo I de Transporte de Electrón / Glutatión / Neuronas Motoras Límite: Animals Idioma: En Revista: Int J Mol Sci Año: 2014 Tipo del documento: Article País de afiliación: Italia

Texto completo: 1 Colección: 01-internacional Asunto principal: Proteínas de Unión a Hierro / Complejo I de Transporte de Electrón / Glutatión / Neuronas Motoras Límite: Animals Idioma: En Revista: Int J Mol Sci Año: 2014 Tipo del documento: Article País de afiliación: Italia