Comprehensive multi-modality imaging approach in arrhythmogenic cardiomyopathy-an expert consensus document of the European Association of Cardiovascular Imaging.
Eur Heart J Cardiovasc Imaging
; 18(3): 237-253, 2017 Mar 01.
Article
en En
| MEDLINE
| ID: mdl-28069601
ABSTRACT
Arrhythmogenic cardiomyopathy (AC) is a progressive disease with high risk of life-threatening ventricular arrhythmias. A genetic mutation is found in up to 50-60% of probands, mostly affecting desmosomal genes. Diagnosis of AC is made by a combination of data from different modalities including imaging, electrocardiogram, Holter monitoring, family history, genetic testing, and tissue properties. Being a progressive cardiomyopathy, repeated cardiac imaging is needed in AC patients. Repeated imaging is important also for risk assessment of ventricular arrhythmias. This expert consensus document gives clinical recommendations for how to use multi-modality imaging in the different aspects of AC disease, including diagnosis, family screening, follow-up, risk assessment, and differential diagnosis.
Palabras clave
Texto completo:
1
Colección:
01-internacional
Asunto principal:
Ecocardiografía
/
Interpretación de Imagen Asistida por Computador
/
Guías de Práctica Clínica como Asunto
/
Displasia Ventricular Derecha Arritmogénica
Tipo de estudio:
Diagnostic_studies
/
Guideline
/
Risk_factors_studies
Límite:
Female
/
Humans
/
Male
País/Región como asunto:
Europa
Idioma:
En
Revista:
Eur Heart J Cardiovasc Imaging
Año:
2017
Tipo del documento:
Article
País de afiliación:
Noruega