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Progressive pulmonary fibrosis in a murine model of Hermansky-Pudlak syndrome.
Abudi-Sinreich, Shachar; Bodine, Steven P; Yokoyama, Tadafumi; Tolman, Nathanial J; Tyrlik, Michal; Testa, Lauren C; Han, Chen G; Dorward, Heidi M; Wincovitch, Stephen M; Anikster, Yair; Gahl, William A; Cinar, Resat; Gochuico, Bernadette R; Malicdan, May Christine V.
Afiliación
  • Abudi-Sinreich S; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Bodine SP; The Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel.
  • Yokoyama T; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Tolman NJ; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Tyrlik M; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA.
  • Testa LC; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Han CG; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA.
  • Dorward HM; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Wincovitch SM; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Anikster Y; National Human Genome Research Institute (NHGRI) Cytogenetics and Microscopy Core, National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Gahl WA; The Sackler School of Medicine, Tel Aviv University, Tel Aviv, Israel.
  • Cinar R; Edmond and Lily Safra Children's Hospital, Sheba Medical Center, Ramat Gan, Israel.
  • Gochuico BR; Human Biochemical Genetics Section, National Human Genome Research Institute (NHGRI), National Institute of Health (NIH), Bethesda, MD, 20892, USA.
  • Malicdan MCV; UDP Translational Laboratory, NIH Undiagnosed Diseases Program, National Human Genome Research Institute (NHGRI), National Institutes of Health (NIH), Bethesda, MD, 20892, USA.
Respir Res ; 23(1): 112, 2022 May 04.
Article en En | MEDLINE | ID: mdl-35509004

Texto completo: 1 Colección: 01-internacional Asunto principal: Síndrome de Hermanski-Pudlak / Fibrosis Pulmonar Idiopática Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Respir Res Año: 2022 Tipo del documento: Article País de afiliación: Estados Unidos

Texto completo: 1 Colección: 01-internacional Asunto principal: Síndrome de Hermanski-Pudlak / Fibrosis Pulmonar Idiopática Tipo de estudio: Prognostic_studies Límite: Animals Idioma: En Revista: Respir Res Año: 2022 Tipo del documento: Article País de afiliación: Estados Unidos