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Outcomes of 38 patients with PFIC3: Impact of genotype and of response to ursodeoxycholic acid therapy.
Gonzales, Emmanuel; Gardin, Antoine; Almes, Marion; Darmellah-Remil, Amaria; Seguin, Hanh; Mussini, Charlotte; Franchi-Abella, Stéphanie; Duché, Mathieu; Ackermann, Oanez; Thébaut, Alice; Habes, Dalila; Hermeziu, Bogdan; Lapalus, Martine; Falguières, Thomas; Combal, Jean-Philippe; Benichou, Bernard; Valero, Sonia; Davit-Spraul, Anne; Jacquemin, Emmanuel.
Afiliación
  • Gonzales E; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Gardin A; Inserm U1193, Hepatinov, University Paris-Saclay, Orsay, France.
  • Almes M; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Darmellah-Remil A; Inserm U1193, Hepatinov, University Paris-Saclay, Orsay, France.
  • Seguin H; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Mussini C; Inserm U1193, Hepatinov, University Paris-Saclay, Orsay, France.
  • Franchi-Abella S; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Duché M; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Ackermann O; Pathology, Bicêtre Hospital, Assistance Publique - Hôpitaux de Paris, University Paris-Saclay, Le Kremlin-Bicêtre, France.
  • Thébaut A; Pediatric Radiology, Bicêtre Hospital, Assistance Publique - Hôpitaux de Paris, University Paris-Saclay, Le Kremlin-Bicêtre, France.
  • Habes D; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Hermeziu B; Pediatric Radiology, Bicêtre Hospital, Assistance Publique - Hôpitaux de Paris, University Paris-Saclay, Le Kremlin-Bicêtre, France.
  • Lapalus M; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Falguières T; Inserm U1193, Hepatinov, University Paris-Saclay, Orsay, France.
  • Combal JP; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Benichou B; Inserm U1193, Hepatinov, University Paris-Saclay, Orsay, France.
  • Valero S; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
  • Davit-Spraul A; Inserm U1193, Hepatinov, University Paris-Saclay, Orsay, France.
  • Jacquemin E; Pediatric Hepatology and Liver Transplantation, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, France.
JHEP Rep ; 5(10): 100844, 2023 Oct.
Article en En | MEDLINE | ID: mdl-37701337

Texto completo: 1 Colección: 01-internacional Tipo de estudio: Prognostic_studies Idioma: En Revista: JHEP Rep Año: 2023 Tipo del documento: Article País de afiliación: Francia

Texto completo: 1 Colección: 01-internacional Tipo de estudio: Prognostic_studies Idioma: En Revista: JHEP Rep Año: 2023 Tipo del documento: Article País de afiliación: Francia