[Primary antibody deficiencies and respiratory manifestations in adults].
Zhonghua Jie He He Hu Xi Za Zhi
; 47(4): 388-392, 2024 Apr 12.
Article
en Zh
| MEDLINE
| ID: mdl-38599818
ABSTRACT
Primary antibody deficiencies (PAD) are a group of congenital disorders caused by genetic defects that affect the development and function of the body's immune defence mechanisms. Patients with PAD may present with recurrent infections, lymphoproliferation, autoimmune diseases, autoinflammation, or malignancies. Respiratory system manifestations may include bronchiectasis, bronchial asthma, and interstitial lung disease, among others. A comprehensive understanding of PADs will help to distinguish these covert cases from more common respiratory diseases.
Texto completo:
1
Colección:
01-internacional
Asunto principal:
Enfermedades Respiratorias
/
Asma
/
Enfermedades Autoinmunes
/
Bronquiectasia
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Enfermedades de Inmunodeficiencia Primaria
Límite:
Adult
/
Humans
Idioma:
Zh
Revista:
Zhonghua Jie He He Hu Xi Za Zhi
Año:
2024
Tipo del documento:
Article
País de afiliación:
China