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ALS-causing mutations differentially affect PGC-1α expression and function in the brain vs. peripheral tissues.
Bayer, Hanna; Lang, Kerstin; Buck, Eva; Higelin, Julia; Barteczko, Lara; Pasquarelli, Noemi; Sprissler, Jasmin; Lucas, Tanja; Holzmann, Karlheinz; Demestre, Maria; Lindenberg, Katrin S; Danzer, Karin M; Boeckers, Tobias; Ludolph, Albert C; Dupuis, Luc; Weydt, Patrick; Witting, Anke.
Afiliação
  • Bayer H; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: hanna.bayer@uni-ulm.de.
  • Lang K; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: Kerstin.lang@uni-ulm.de.
  • Buck E; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: eva.buck@uni-ulm.de.
  • Higelin J; Institute of Anatomy and Cell Biology, Ulm University, Ulm, DE 89081, Germany. Electronic address: Julia.higelin@uni-ulm.de.
  • Barteczko L; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: Lara.barteczko@uni-ulm.de.
  • Pasquarelli N; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: Noemi.pasquarelli@uni-ulm.de.
  • Sprissler J; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: Jasmin.sprissler@uni-ulm.de.
  • Lucas T; Department of Gene Therapy, Ulm University, Ulm, DE 89081, Germany. Electronic address: Tanjalucas@web.de.
  • Holzmann K; Genomics Core Facility, Ulm University, Ulm, DE 89081, Germany. Electronic address: karlheinz.holzmann@uni-ulm.de.
  • Demestre M; Institute of Anatomy and Cell Biology, Ulm University, Ulm, DE 89081, Germany. Electronic address: maria.demestre@uni-ulm.de.
  • Lindenberg KS; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: katrin.lindenberg@uni-ulm.de.
  • Danzer KM; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: karin.danzer@uni-ulm.de.
  • Boeckers T; Institute of Anatomy and Cell Biology, Ulm University, Ulm, DE 89081, Germany. Electronic address: tobias.boeckers@uni-ulm.de.
  • Ludolph AC; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: albert.ludolph@uni-ulm.de.
  • Dupuis L; INSERM U1118, F 67085, France; Université de Strasbourg, fédération de Médecine Translationnelle, F 67085, France. Electronic address: ldupuis@neuro-cnrs.unistra.fr.
  • Weydt P; Department of Neurology, Ulm University, DE 89081, Germany; Department of Neurodegenerative Disorders and Gerontopsychiatry, University of Bonn, 53127 Bonn, Germany. Electronic address: patrick.weydt@uni-bonn.de.
  • Witting A; Department of Neurology, Ulm University, DE 89081, Germany. Electronic address: anke.witting@uni-ulm.de.
Neurobiol Dis ; 97(Pt A): 36-45, 2017 01.
Article em En | MEDLINE | ID: mdl-27818323

Texto completo: 1 Coleções: 01-internacional Temas: Geral Base de dados: MEDLINE Assunto principal: Encéfalo / Proteína FUS de Ligação a RNA / Superóxido Dismutase-1 / Coativador 1-alfa do Receptor gama Ativado por Proliferador de Peroxissomo / Esclerose Lateral Amiotrófica Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Neurobiol Dis Assunto da revista: NEUROLOGIA Ano de publicação: 2017 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Temas: Geral Base de dados: MEDLINE Assunto principal: Encéfalo / Proteína FUS de Ligação a RNA / Superóxido Dismutase-1 / Coativador 1-alfa do Receptor gama Ativado por Proliferador de Peroxissomo / Esclerose Lateral Amiotrófica Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Neurobiol Dis Assunto da revista: NEUROLOGIA Ano de publicação: 2017 Tipo de documento: Article