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Recovery of natural killer cell cytotoxicity in a p.A91V perforin homozygous patient following severe haemophagocytic lymphohistiocytosis.
Jang, Helena S; Flinsenberg, Thijs W H; Lacaze, Paul; Thia, Kevin Y T; Noori, Tahereh; Fernando, Suran L; Kerridge, Ian; Riaz, Moeen; McNeil, John J; Blombery, Piers A; Trapani, Joseph A; Voskoboinik, Ilia.
Afiliação
  • Jang HS; Immunorheumatology Laboratory, New South Wales Health Pathology, Royal North Shore Hospital, Sydney, Australia.
  • Flinsenberg TWH; Department of Clinical Immunology and Allergy, Royal North Shore Hospital, Sydney, Australia.
  • Lacaze P; Cancer Immunology Program, Killer Cell Biology Laboratory, Peter MacCallum Cancer Centre, Melbourne, VIC, Australia.
  • Thia KYT; Department of Epidemiology and Preventive Medicine, School of Public Health and Preventive Medicine, Monash University, Melbourne, VIC, Australia.
  • Noori T; Cancer Immunology Program, Cancer Cell Death Laboratory, Peter MacCallum Cancer Centre, Melbourne, VIC, Australia.
  • Fernando SL; Cancer Immunology Program, Killer Cell Biology Laboratory, Peter MacCallum Cancer Centre, Melbourne, VIC, Australia.
  • Kerridge I; Immunorheumatology Laboratory, New South Wales Health Pathology, Royal North Shore Hospital, Sydney, Australia.
  • Riaz M; Department of Clinical Immunology and Allergy, Royal North Shore Hospital, Sydney, Australia.
  • McNeil JJ; The University of Sydney, Sydney, Australia.
  • Blombery PA; Department of Haematology, Royal North Shore Hospital, Sydney, Australia.
  • Trapani JA; Department of Epidemiology and Preventive Medicine, School of Public Health and Preventive Medicine, Monash University, Melbourne, VIC, Australia.
  • Voskoboinik I; Department of Epidemiology and Preventive Medicine, School of Public Health and Preventive Medicine, Monash University, Melbourne, VIC, Australia.
Br J Haematol ; 190(3): 458-461, 2020 08.
Article em En | MEDLINE | ID: mdl-32342501

Texto completo: 1 Coleções: 01-internacional Temas: Geral Base de dados: MEDLINE Assunto principal: Células Matadoras Naturais / Linfo-Histiocitose Hemofagocítica / Perforina Tipo de estudo: Etiology_studies Limite: Adult / Humans / Male Idioma: En Revista: Br J Haematol Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Austrália

Texto completo: 1 Coleções: 01-internacional Temas: Geral Base de dados: MEDLINE Assunto principal: Células Matadoras Naturais / Linfo-Histiocitose Hemofagocítica / Perforina Tipo de estudo: Etiology_studies Limite: Adult / Humans / Male Idioma: En Revista: Br J Haematol Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Austrália