Abdominal Imaging of Children and Young Adults With Fontan Circulation: Pathophysiology and Surveillance.
AJR Am J Roentgenol
; 217(1): 207-217, 2021 07.
Article
em En
| MEDLINE
| ID: mdl-33909464
ABSTRACT
OBJECTIVE. The Fontan procedure has significantly improved the survival in children with a functional single ventricle, but it is associated with chronically elevated systemic venous pressure that leads to multisystemic complications. Imaging plays an important role in assessing these complications and guiding management. The pathophysiology, imaging modalities, and current surveillance recommendations are discussed and illustrated. CONCLUSION. Significant improvement in survival of patients with Fontan circulation is associated with ongoing cardiac and extracardiac comorbidities and multisystemic complications. The liver and intestines are particularly vulnerable to damage. In addition, this patient population has been shown to be at increased risk of certain malignancies such as hepatocellular carcinoma and neuroendocrine tumors. Familiarity with imaging findings of Fontan-associated liver disease and other abdominal complications of the Fontan circulation is essential for radiologists because we are likely to encounter these patients in our general practice.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Temas:
Geral
Base de dados:
MEDLINE
Assunto principal:
Complicações Pós-Operatórias
/
Enteropatias Perdedoras de Proteínas
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Imageamento por Ressonância Magnética
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Técnica de Fontan
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Nefropatias
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Hepatopatias
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Doenças Linfáticas
Tipo de estudo:
Etiology_studies
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Guideline
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Screening_studies
Limite:
Adolescent
/
Child
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Female
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Humans
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Male
Idioma:
En
Revista:
AJR Am J Roentgenol
Ano de publicação:
2021
Tipo de documento:
Article
País de afiliação:
Canadá