Myxoinflammatory Fibroblastic Sarcoma.
Surg Pathol Clin
; 17(1): 83-96, 2024 Mar.
Article
em En
| MEDLINE
| ID: mdl-38278610
ABSTRACT
MIFS is a low-grade fibroblastic sarcoma that predilects to superficial distal extremity soft tissue. It is composed of plump spindled and epithelioid cells, inflammatory infiltrates, and mucin deposits in a fibrosclerotic stroma. Large epithelioid cells harboring bizarre nuclei and virocyte-like macronucleoli and pleomorphic pseudolipoblasts are characteristic. While conventional MIFS has locally recurrent potential but minimal metastatic risk, tumors with high-grade histologic features have a greater risk for recurrence and metastasis. Wide local excision is the recommended treatment.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Temas:
Geral
/
Tipos_de_cancer
/
Pele
Base de dados:
MEDLINE
Assunto principal:
Sarcoma
/
Neoplasias Cutâneas
/
Neoplasias de Tecidos Moles
/
Fibrossarcoma
Tipo de estudo:
Diagnostic_studies
Limite:
Humans
Idioma:
En
Revista:
Surg Pathol Clin
Ano de publicação:
2024
Tipo de documento:
Article
País de afiliação:
Estados Unidos