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Abdominal wall congenital infantile fibrosarcoma: A rare case report and literature review.
Yaynishet, Yodit Abraham; Salah, Fathia Omer; Derbew, Hermon Miliard; Hailu, Abel; Fufa, Diriba; Abafogi, Abdo Kedir; Alemu, Hailu.
Afiliação
  • Yaynishet YA; Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.
  • Salah FO; Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.
  • Derbew HM; Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.
  • Hailu A; Childrens Hospital of Philadelphia, Department of Radiology, Philadelphia, PA, USA.
  • Fufa D; Addis Ababa University, College of Health Sciences, Department of Pediatric Hematology/Oncology, Addis Ababa, Ethiopia.
  • Abafogi AK; Jimma University, Department of Pediatric and Child Health, Jimma, Ethiopia.
  • Alemu H; Jimma University, Department of Pathology, Jimma, Ethiopia.
Radiol Case Rep ; 19(8): 3176-3179, 2024 Aug.
Article em En | MEDLINE | ID: mdl-38779193
ABSTRACT
Congenital infantile fibrosarcoma is a rare malignant soft tissue tumor, accounting for less than 1%-2% of childhood cancers. Although it can arise from any body part, an abdominal wall origin is exceptionally rare. This case report presents a case of congenital infantile fibrosarcoma originating from the abdominal wall. To the best of our knowledge, this is only the second reported case of abdominal wall congenital infantile fibrosarcoma. Unlike adult fibrosarcoma, infantile fibrosarcoma has a good prognosis with less metastasis. Early diagnosis and management are critical for improving outcomes in such rare cases.
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Texto completo: 1 Coleções: 01-internacional Temas: Geral Base de dados: MEDLINE Idioma: En Revista: Radiol Case Rep / Radiology case reports Ano de publicação: 2024 Tipo de documento: Article País de afiliação: Etiópia

Texto completo: 1 Coleções: 01-internacional Temas: Geral Base de dados: MEDLINE Idioma: En Revista: Radiol Case Rep / Radiology case reports Ano de publicação: 2024 Tipo de documento: Article País de afiliação: Etiópia