Homocystinuria presenting with portal vein thrombosis and pancreatic pseudocyst: a case report.
Pediatr Radiol
; 27(10): 802-4, 1997 Oct.
Article
em En
| MEDLINE
| ID: mdl-9323245
ABSTRACT
Homocystinuria is a rare, inherited metabolic disease frequently associated with severe multisystemic involvement such as dislocated lenses, skeletal deformities, mental retardation, and premature vascular occlusion. Arterial and venous thromboembolic events present frequent and life-threatening complications in homocystinuric patients. It has been suggested that mild homocystinemia would be a risk factor for vascular disease.
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Coleções:
01-internacional
Temas:
Geral
/
Tipos_de_cancer
/
Outros_tipos
Base de dados:
MEDLINE
Assunto principal:
Pseudocisto Pancreático
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Veia Porta
/
Tromboflebite
/
Homocistinúria
Tipo de estudo:
Diagnostic_studies
/
Observational_studies
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Prognostic_studies
/
Risk_factors_studies
Limite:
Child
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Female
/
Humans
Idioma:
En
Revista:
Pediatr Radiol
Ano de publicação:
1997
Tipo de documento:
Article