1.
J Inherit Metab Dis
; 27(1): 111-2, 2004.
Artigo
em Inglês
| MEDLINE
| ID: mdl-15065575
RESUMO
Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.