Detalhe da pesquisa
1.
Dynamic use of historical controls in clinical trials for rare disease research: A re-evaluation of the MILES trial.
Clin Trials
; 20(3): 223-234, 2023 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-36927115
2.
Wilms Tumor 1-Driven Fibroblast Activation and Subpleural Thickening in Idiopathic Pulmonary Fibrosis.
Int J Mol Sci
; 24(3)2023 Feb 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-36769178
3.
Machine learning can predict disease manifestations and outcomes in lymphangioleiomyomatosis.
Eur Respir J
; 57(6)2021 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-33303533
4.
Single-Cell Transcriptomic Analysis Identifies a Unique Pulmonary Lymphangioleiomyomatosis Cell.
Am J Respir Crit Care Med
; 202(10): 1373-1387, 2020 11 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-32603599
5.
Eight novel variants in the SLC34A2 gene in pulmonary alveolar microlithiasis.
Eur Respir J
; 55(2)2020 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-31831582
6.
Pulmonary Alveolar Microlithiasis.
Semin Respir Crit Care Med
; 41(2): 280-287, 2020 Apr.
Artigo
em Inglês
| MEDLINE | ID: mdl-32279298
7.
Mitogenic stimulation accelerates influenza-induced mortality by increasing susceptibility of alveolar type II cells to infection.
Proc Natl Acad Sci U S A
; 114(32): E6613-E6622, 2017 08 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-28739896
8.
Lymphangioleiomyomatosis: A Monogenic Model of Malignancy.
Annu Rev Med
; 68: 69-83, 2017 01 14.
Artigo
em Inglês
| MEDLINE | ID: mdl-28099079
9.
Analysis of the MILES cohort reveals determinants of disease progression and treatment response in lymphangioleiomyomatosis.
Eur Respir J
; 53(4)2019 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-30846465
10.
NKG2D Regulation of Lung Pathology and Dendritic Cell Function Following Respiratory Syncytial Virus Infection.
J Infect Dis
; 218(11): 1822-1832, 2018 10 20.
Artigo
em Inglês
| MEDLINE | ID: mdl-29554301
11.
The vitamin D binding protein axis modifies disease severity in lymphangioleiomyomatosis.
Eur Respir J
; 52(5)2018 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-30093573
12.
Lymphangioleiomyomatosis Diagnosis and Management: High-Resolution Chest Computed Tomography, Transbronchial Lung Biopsy, and Pleural Disease Management. An Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guideline.
Am J Respir Crit Care Med
; 196(10): 1337-1348, 2017 11 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-29140122
13.
Dendritic Cell Trafficking and Function in Rare Lung Diseases.
Am J Respir Cell Mol Biol
; 57(4): 393-402, 2017 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-28586276
14.
Differential Ligand Binding Specificities of the Pulmonary Collectins Are Determined by the Conformational Freedom of a Surface Loop.
Biochemistry
; 56(31): 4095-4105, 2017 08 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-28719181
15.
Official American Thoracic Society/Japanese Respiratory Society Clinical Practice Guidelines: Lymphangioleiomyomatosis Diagnosis and Management.
Am J Respir Crit Care Med
; 194(6): 748-61, 2016 09 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-27628078
16.
Unsupervised gene expression analyses identify IPF-severity correlated signatures, associated genes and biomarkers.
BMC Pulm Med
; 17(1): 133, 2017 Oct 20.
Artigo
em Inglês
| MEDLINE | ID: mdl-29058630
17.
Epidemiology of Rare Lung Diseases: The Challenges and Opportunities to Improve Research and Knowledge.
Adv Exp Med Biol
; 1031: 419-442, 2017.
Artigo
em Inglês
| MEDLINE | ID: mdl-29214586
18.
Elucidation of Lipid Binding Sites on Lung Surfactant Protein A Using X-ray Crystallography, Mutagenesis, and Molecular Dynamics Simulations.
Biochemistry
; 55(26): 3692-701, 2016 07 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-27324153
19.
Keratinocyte growth factor administration attenuates murine pulmonary mycobacterium tuberculosis infection through granulocyte-macrophage colony-stimulating factor (GM-CSF)-dependent macrophage activation and phagolysosome fusion.
J Biol Chem
; 290(11): 7151-9, 2015 Mar 13.
Artigo
em Inglês
| MEDLINE | ID: mdl-25605711
20.
Keratinocyte growth factor supports pulmonary innate immune defense through maintenance of alveolar antimicrobial protein levels and macrophage function.
Am J Physiol Lung Cell Mol Physiol
; 310(9): L868-79, 2016 05 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-26919897