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1.
Nutritional interventions in primary mitochondrial disorders: Developing an evidence base.
Mol Genet Metab
; 119(3): 187-206, 2016 11.
Article
in English
| MEDLINE | ID: mdl-27665271
2.
Computational modeling to predict nitrogen balance during acute metabolic decompensation in patients with urea cycle disorders.
J Inherit Metab Dis
; 39(1): 17-24, 2016 Jan.
Article
in English
| MEDLINE | ID: mdl-26260782
3.
Breakfast with glycomacropeptide compared with amino acids suppresses plasma ghrelin levels in individuals with phenylketonuria.
Mol Genet Metab
; 100(4): 303-8, 2010 Aug.
Article
in English
| MEDLINE | ID: mdl-20466571
4.
Nutritional Management of Phenylketonuria.
Ann Nestle Eng
; 68(2): 58-69, 2010 Jun.
Article
in English
| MEDLINE | ID: mdl-22475869
5.
Reassessment of phenylalanine tolerance in adults with phenylketonuria is needed as body mass changes.
Mol Genet Metab
; 98(4): 331-7, 2009 Dec.
Article
in English
| MEDLINE | ID: mdl-19747868
6.
Purification and use of glycomacropeptide for nutritional management of phenylketonuria.
J Food Sci
; 74(4): E199-206, 2009.
Article
in English
| MEDLINE | ID: mdl-19490325
7.
Improved nutritional management of phenylketonuria by using a diet containing glycomacropeptide compared with amino acids.
Am J Clin Nutr
; 89(4): 1068-77, 2009 Apr.
Article
in English
| MEDLINE | ID: mdl-19244369
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