1.
J Paediatr Child Health
; 48(3): E122-5, 2012 Mar.
Artículo
en Inglés
| MEDLINE
| ID: mdl-22050445
RESUMEN
Acute liver failure (ALF) with macrophage activation syndrome (MAS) is well known as a complication of systemic-onset juvenile idiopathic arthritis (S-JIA). However, liver failure without overt MAS is rare in S-JIA. We encountered two Japanese children with S-JIA in whom ALF developed during the remission of clinical manifestations. ALF without MAS was improved with plasma exchange and cyclosporine A combined with pulse methylprednisolone.