RESUMEN
We report a case of 67 year-old female with a 48-year survival of a Starr-Edwards valve at mitral position. The patient underwent Starr-Edwards mitral valve replacement at age of 19 years for mitral stenosis secondary to severe rheumatic valve disease. The patient had experienced a progressive decline in her functional status with increasing dyspnoea on exertion over a two-week period to eventual development of severe shortness of breath at rest prior to hospitalisation. Transoesophageal echocardiogram revealed severe para-prosthetic and intravalvular mitral valve regurgitation. The patient underwent explantation of Starr-Edwards valve and replacement with a mechanical prosthesis. Our case details the longest reported survival of a Starr-Edwards prosthetic valve at mitral area.
Asunto(s)
Ecocardiografía Transesofágica , Implantación de Prótesis de Válvulas Cardíacas , Prótesis Valvulares Cardíacas , Insuficiencia de la Válvula Mitral , Válvula Mitral , Femenino , Estudios de Seguimiento , Humanos , Persona de Mediana Edad , Válvula Mitral/diagnóstico por imagen , Válvula Mitral/ultraestructura , Insuficiencia de la Válvula Mitral/diagnóstico por imagen , Insuficiencia de la Válvula Mitral/cirugía , Factores de TiempoRESUMEN
A 46-year-old male was diagnosed with hypertrophic cardiomyopathy (HCM) and severe left ventricular outflow tract (LVOT) obstruction. Genetic testing revealed that this was a "mimic of HCM" and the true diagnosis was Fabry's disease, although there were no other clinical features of Fabry's. Despite maximal medical therapy he remained symptomatic from the outflow tract gradient and required surgical myectomy for symptom relief. This case illustrates the diagnosis of an HCM mimic by genetic testing.
Asunto(s)
Procedimientos Quirúrgicos Cardíacos , Enfermedad de Fabry/diagnóstico , Enfermedad de Fabry/terapia , Pruebas Genéticas/métodos , Obstrucción del Flujo Ventricular Externo/diagnóstico , Obstrucción del Flujo Ventricular Externo/terapia , Cardiomiopatía Hipertrófica , Diagnóstico Diferencial , Ecocardiografía , Electrocardiografía , Enfermedad de Fabry/complicaciones , Enfermedad de Fabry/genética , Humanos , Masculino , Persona de Mediana Edad , Mutación Puntual , Obstrucción del Flujo Ventricular Externo/complicaciones , Obstrucción del Flujo Ventricular Externo/genética , alfa-Galactosidasa/administración & dosificación , alfa-Galactosidasa/genéticaAsunto(s)
Absceso/complicaciones , Manejo de la Vía Aérea/métodos , Oxigenación por Membrana Extracorpórea , Enfermedades Faríngeas/complicaciones , Supraglotitis/complicaciones , Absceso/cirugía , Servicio de Urgencia en Hospital , Femenino , Humanos , Intubación Intratraqueal , Persona de Mediana Edad , Planificación de Atención al Paciente , Enfermedades Faríngeas/cirugía , TraqueostomíaRESUMEN
Accidental hypothermia can lead to untoward cardiac manifestations and arrest. This report presents a case series of severe accidental hypothermia with cardiac complications in three emergency patients who were treated with extracorporeal membrane oxygenation (ECMO) and survived after re-warming. The aim of this discussion was to encourage more clinicians to consider ECMO as a re-warming therapy for severe hypothermia with circulatory collapse and to prompt discussion about decreasing the barriers to its use. Niehaus MT , Pechulis RM , Wu JK , Frei S , Hong JJ , Sandhu RS , Greenberg MR . Extracorporeal membrane oxygenation (ECMO) for hypothermic cardiac deterioration: a case series. Prehosp Disaster Med. 2016;31(5):570-571.
Asunto(s)
Oxigenación por Membrana Extracorpórea , Paro Cardíaco/terapia , Hipotermia/terapia , Adulto , Femenino , Humanos , Masculino , Factores de Tiempo , Resultado del Tratamiento , Adulto JovenRESUMEN
We report results on lithium alumino-silicate ion source development in preparation for warm dense matter heating experiments on the new neutralized drift compression experiment II. The practical limit to the current density for a lithium alumino-silicate source is determined by the maximum operating temperature that the ion source can withstand before running into problems of heat transfer, melting of the alumino-silicate material, and emission lifetime. Using small prototype emitters, at a temperature of ≈1275 °C, a space-charge limited Li(+) beam current density of J ≈1 mA/cm(2) was obtained. The lifetime of the ion source was ≈50 h while pulsing at a rate of 0.033 Hz with a pulse duration of 5-6 µs.