Juvenile xanthogranuloma--a rare cause of unilateral orbital swelling in an elderly patient.

OBJECTIVE: To report the clinical and pathologic features of an elderly patient with a unilateral orbital swelling and proptosis caused by Juvenile Xanthogranuloma diagnosed and confirmed by orbital biopsy. DESIGN: Interventional case report. PARTICIPANTS: One patient. INTERVENTION: Steroids (Medrol dose pack) and radiation. MAIN OUTCOME MEASURES: Unusual clinical presentation and pathological features of Juvenile Xanthogranuloma in the orbit. CONCLUSIONS: Juvenile Xanthogranuloma affecting one orbit is very rare with unilateral involvement in an elderly patient. Steroids and radiation therapy were very effective in treatment and provided impressive results.