RESUMO
A variant of Mounier-Kuhn syndrome is reported where the patient had bronchiectasis with tracheo-bronchomegaly. The patient also had facial anomalies and asthenozoospermia. This combination has not been reported so far in the literature.
Assuntos
Traqueobroncomegalia/diagnóstico , Adulto , Bronquiectasia/complicações , Fácies , Humanos , Infertilidade Masculina/complicações , Masculino , Traqueobroncomegalia/complicaçõesRESUMO
Twelve patients of elapid ophitoxaemia presented with neuromuscular paralytic features were given anticholinesterase (Neostigmine) in recommended dosage. In four of these patients, despite neuromuscular paralysis, no ASV was used. All these four patients survived. In eight patients, ASV was used; in three of whom it used in doses less than 50 units, yet patients survived. Of the remaining five, despite use of ASV in higher doses (more than 50 units), two succumbed to death. Eight patients required ventilatory support. Hence, in absence of any definite role of ASV in management of elapid ophitoxaemia (snake bite), use of anticholinesterase drugs alone, with good supportive care and prevention of likely complications, can result in satisfactory outcome.
Assuntos
Antivenenos/uso terapêutico , Venenos Elapídicos/antagonistas & inibidores , Elapidae , Mordeduras de Serpentes/terapia , Adolescente , Adulto , Animais , Antivenenos/administração & dosagem , Inibidores da Colinesterase/administração & dosagem , Inibidores da Colinesterase/uso terapêutico , Feminino , Seguimentos , Humanos , Índia , Masculino , Neostigmina/administração & dosagem , Neostigmina/uso terapêutico , Doenças Neuromusculares/tratamento farmacológico , Doenças Neuromusculares/terapia , Paralisia/tratamento farmacológico , Paralisia/terapia , Respiração Artificial , Mordeduras de Serpentes/tratamento farmacológico , Taxa de Sobrevida , Resultado do TratamentoAssuntos
Síndrome da Retração Ocular/patologia , Oftalmoplegia/patologia , Adulto , Feminino , Humanos , MasculinoAssuntos
Inseticidas/intoxicação , Compostos Organofosforados , Doença Aguda , Adulto , Feminino , Humanos , Masculino , PrognósticoRESUMO
This report deals with a young girl with Duane's retraction syndrome who also had left facial hemiatrophy (Parry-Romberg syndrome). Report of such an association is probably first of its type to be documented in literature.