Detalhe da pesquisa
1.
How the central domain of dystrophin acts to bridge F-actin to sarcolemmal lipids.
J Struct Biol
; 209(1): 107411, 2020 01 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-31689503
2.
Dystrophin's central domain forms a complex filament that becomes disorganized by in-frame deletions.
J Biol Chem
; 293(18): 6637-6646, 2018 05 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-29535188
3.
Human Dystrophin Structural Changes upon Binding to Anionic Membrane Lipids.
Biophys J
; 115(7): 1231-1239, 2018 10 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-30197181
4.
Dystrophin and Spectrin, Two Highly Dissimilar Sisters of the Same Family.
Subcell Biochem
; 82: 373-403, 2017.
Artigo
em Inglês
| MEDLINE | ID: mdl-28101868
5.
Becker muscular dystrophy severity is linked to the structure of dystrophin.
Hum Mol Genet
; 24(5): 1267-79, 2015 Mar 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-25348330
6.
Contrast-Matched Isotropic Bicelles: A Versatile Tool to Specifically Probe the Solution Structure of Peripheral Membrane Proteins Using SANS.
Langmuir
; 33(26): 6572-6580, 2017 07 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-28581294
7.
IgA Structure Variations Associate with Immune Stimulations and IgA Mesangial Deposition.
J Am Soc Nephrol
; 27(9): 2748-61, 2016 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-26825533
8.
Dystrophin Hot-Spot Mutants Leading to Becker Muscular Dystrophy Insert More Deeply into Membrane Models than the Native Protein.
Biochemistry
; 55(29): 4018-26, 2016 07 26.
Artigo
em Inglês
| MEDLINE | ID: mdl-27367833
9.
Structural Basis of Neuronal Nitric-oxide Synthase Interaction with Dystrophin Repeats 16 and 17.
J Biol Chem
; 290(49): 29531-41, 2015 Dec 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-26378238
10.
Clinical phenotypes as predictors of the outcome of skipping around DMD exon 45.
Ann Neurol
; 77(4): 668-74, 2015 Apr.
Artigo
em Inglês
| MEDLINE | ID: mdl-25612243
11.
Cholesterol favors the anchorage of human dystrophin repeats 16 to 21 in membrane at physiological surface pressure.
Biochim Biophys Acta
; 1838(5): 1266-73, 2014 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-24440661
12.
The spectrin family of proteins: a unique coiled-coil fold for various molecular surface properties.
J Struct Biol
; 186(3): 392-401, 2014 Jun.
Artigo
em Inglês
| MEDLINE | ID: mdl-24657228
13.
Resisting sarcolemmal rupture: dystrophin repeats increase membrane-actin stiffness.
FASEB J
; 27(1): 359-67, 2013 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-23033320
14.
Molecular clues about the dystrophin-neuronal nitric oxide synthase interaction: a theoretical approach.
Biochemistry
; 52(44): 7777-84, 2013 Nov 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-24063785
15.
Novel mutation in spectrin-like repeat 1 of dystrophin central domain causes protein misfolding and mild Becker muscular dystrophy.
J Biol Chem
; 287(22): 18153-62, 2012 May 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-22453924
16.
Exon edited dystrophin rods in the hinge 3 region.
Biochim Biophys Acta
; 1824(10): 1080-9, 2012 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-22750404
17.
Spectrin-like repeats 11-15 of human dystrophin show adaptations to a lipidic environment.
J Biol Chem
; 286(35): 30481-30491, 2011 Sep 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-21712383
18.
Systemic delivery of allogenic muscle stem cells induces long-term muscle repair and clinical efficacy in duchenne muscular dystrophy dogs.
Am J Pathol
; 179(5): 2501-18, 2011 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-21924229
19.
Abnormal functional lateralization and activity of language brain areas in typical specific language impairment (developmental dysphasia).
Brain
; 134(Pt 10): 3044-58, 2011 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-21719430
20.
Dystrophin: more than just the sum of its parts.
Biochim Biophys Acta
; 1804(9): 1713-22, 2010 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-20472103