Detalhe da pesquisa
1.
Open ADAMTS13, induced by antibodies, is a biomarker for subclinical immune-mediated thrombotic thrombocytopenic purpura.
Blood
; 136(3): 353-361, 2020 07 16.
Artigo
em Inglês
| MEDLINE | ID: mdl-32356859
2.
N-acetylcysteine in preclinical mouse and baboon models of thrombotic thrombocytopenic purpura.
Blood
; 129(8): 1030-1038, 2017 02 23.
Artigo
em Inglês
| MEDLINE | ID: mdl-28011677
3.
Generation of anti-idiotypic antibodies to detect anti-spacer antibody idiotopes in acute thrombotic thrombocytopenic purpura patients.
Haematologica
; 104(6): 1268-1276, 2019 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-30523052
4.
Child-onset thrombotic thrombocytopenic purpura caused by p.R498C and p.G259PfsX133 mutations in ADAMTS13.
Eur J Haematol
; 2018 May 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-29763513
5.
Long-Term Prevention of Congenital Thrombotic Thrombocytopenic Purpura in ADAMTS13 Knockout Mice by Sleeping Beauty Transposon-Mediated Gene Therapy.
Arterioscler Thromb Vasc Biol
; 37(5): 836-844, 2017 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-28254814
6.
Platelet-derived VWF is not essential for normal thrombosis and hemostasis but fosters ischemic stroke injury in mice.
Blood
; 126(14): 1715-22, 2015 Oct 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-26209660
7.
Inhibition of von Willebrand factor-platelet glycoprotein Ib interaction prevents and reverses symptoms of acute acquired thrombotic thrombocytopenic purpura in baboons.
Blood
; 120(17): 3611-4, 2012 Oct 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-22855603
8.
Thrombotic thrombocytopenic purpura directly linked with ADAMTS13 inhibition in the baboon (Papio ursinus).
Blood
; 116(12): 2005-10, 2010 Sep 23.
Artigo
em Inglês
| MEDLINE | ID: mdl-20551375
9.
ADAMTS13 inhibition to treat acquired von Willebrand syndrome during mechanical circulatory support device implantation.
J Thromb Haemost
; 20(12): 2797-2809, 2022 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-36128768
10.
Mutation of the H-bond acceptor S119 in the ADAMTS13 metalloprotease domain reduces secretion and substrate turnover in a patient with congenital thrombotic thrombocytopenic purpura.
Blood
; 114(21): 4749-52, 2009 Nov 19.
Artigo
em Inglês
| MEDLINE | ID: mdl-19786614
11.
Antithrombin p.Thr147Ala: The First Founder Mutation in People of African Origin Responsible for Inherited Antithrombin Deficiency.
Thromb Haemost
; 121(2): 182-191, 2021 Feb.
Artigo
em Inglês
| MEDLINE | ID: mdl-32920809
12.
Antibodies that conformationally activate ADAMTS13 allosterically enhance metalloprotease domain function.
Blood Adv
; 4(6): 1072-1080, 2020 03 24.
Artigo
em Inglês
| MEDLINE | ID: mdl-32196558
13.
von Willebrand factor increases in experimental cerebral malaria but is not essential for late-stage pathogenesis in mice.
J Thromb Haemost
; 18(9): 2377-2390, 2020 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-32485089
14.
Anti-ADAMTS13 autoantibodies in immune-mediated thrombotic thrombocytopenic purpura do not hamper ELISA-based quantification of ADAMTS13 antigen.
J Thromb Haemost
; 18(4): 985-990, 2020 04.
Artigo
em Inglês
| MEDLINE | ID: mdl-31989742
15.
Restoration of plasma von Willebrand factor deficiency is sufficient to correct thrombus formation after gene therapy for severe von Willebrand disease.
Arterioscler Thromb Vasc Biol
; 28(9): 1621-6, 2008 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-18556568
16.
Differences in von Willebrand factor function in type 2A von Willebrand disease and left ventricular assist device-induced acquired von Willebrand syndrome.
Res Pract Thromb Haemost
; 2(4): 762-766, 2018 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-30397685
17.
Anti-ADAMTS13 Antibodies and a Novel Heterozygous p.R1177Q Mutation in a Case of Pregnancy-Onset Immune-Mediated Thrombotic Thrombocytopenic Purpura.
TH Open
; 2(1): e8-e15, 2018 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-31249923
18.
Anti-ADAMTS13 Autoantibodies against Cryptic Epitopes in Immune-Mediated Thrombotic Thrombocytopenic Purpura.
Thromb Haemost
; 118(10): 1729-1742, 2018 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-30235483
19.
The A/T1381 polymorphism in the A1-domain of von Willebrand factor influences the affinity of von Willebrand factor for platelet glycoprotein Ibalpha.
Thromb Haemost
; 98(1): 178-85, 2007 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-17598011
20.
False positive results in chimeraplasty for von Willebrand Disease.
Thromb Res
; 119(1): 93-104, 2007.
Artigo
em Inglês
| MEDLINE | ID: mdl-16457874