Detalhe da pesquisa
1.
Spontaneous generation of prions and transmissible PrP amyloid in a humanised transgenic mouse model of A117V GSS.
PLoS Biol
; 18(6): e3000725, 2020 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-32516343
2.
A naturally occurring variant of the human prion protein completely prevents prion disease.
Nature
; 522(7557): 478-81, 2015 Jun 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-26061765
3.
Transmission Properties of Human PrP 102L Prions Challenge the Relevance of Mouse Models of GSS.
PLoS Pathog
; 11(7): e1004953, 2015 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-26135918
4.
Inherited prion disease A117V is not simply a proteinopathy but produces prions transmissible to transgenic mice expressing homologous prion protein.
PLoS Pathog
; 9(9): e1003643, 2013.
Artigo
em Inglês
| MEDLINE | ID: mdl-24086135
5.
Progressive neuronal inclusion formation and axonal degeneration in CHMP2B mutant transgenic mice.
Brain
; 135(Pt 3): 819-32, 2012 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-22366797
6.
Absence of spontaneous disease and comparative prion susceptibility of transgenic mice expressing mutant human prion proteins.
J Gen Virol
; 90(Pt 3): 546-558, 2009 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-19218199