Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease): two case reports.
Int J Pediatr Otorhinolaryngol
; 61(3): 243-7, 2001 Dec 01.
Article
en En
| MEDLINE
| ID: mdl-11700194
ABSTRACT
Sinus histiocytosis with massive lymphadenopathy or Destombes-Rosai-Dorfman's syndrome is a rare benign disease of unknown etiology, usually seen in younger patients. The cases reported concerned a 15-month old Caucasian boy and an 8 year old black boy with unilateral cervical enlargement, occasional fever and without any extranodal involvement. Diagnosis was performed by superficial lymph node biopsy. No immunodeficiency was found. The patients received no therapy and a complete spontaneous resolution was seen after a few months in the two cases. The clinical presentation, histologic characteristics, pathogenesis and treatment of the Destombes-Rosai-Dorfman's syndrome are discussed.
Buscar en Google
Bases de datos:
MEDLINE
Asunto principal:
Histiocitosis Sinusal
Límite:
Child
/
Humans
/
Infant
/
Male
Idioma:
En
Revista:
Int J Pediatr Otorhinolaryngol
Año:
2001
Tipo del documento:
Article
País de afiliación:
Marruecos