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Polyglutamine- and temperature-dependent conformational rigidity in mutant huntingtin revealed by immunoassays and circular dichroism spectroscopy.
Fodale, Valentina; Kegulian, Natalie C; Verani, Margherita; Cariulo, Cristina; Azzollini, Lucia; Petricca, Lara; Daldin, Manuel; Boggio, Roberto; Padova, Alessandro; Kuhn, Rainer; Pacifici, Robert; Macdonald, Douglas; Schoenfeld, Ryan C; Park, Hyunsun; Isas, J Mario; Langen, Ralf; Weiss, Andreas; Caricasole, Andrea.
Afiliación
  • Fodale V; IRBM Promidis, Pomezia, Rome, Italy.
  • Kegulian NC; Department of Biochemistry and Molecular Biology, Zilkha Neurogenetic Institute, Keck School of Medicine, University of Southern California, Los Angeles, California, United States of America.
  • Verani M; IRBM Promidis, Pomezia, Rome, Italy.
  • Cariulo C; IRBM Promidis, Pomezia, Rome, Italy.
  • Azzollini L; IRBM Promidis, Pomezia, Rome, Italy.
  • Petricca L; IRBM Promidis, Pomezia, Rome, Italy.
  • Daldin M; IRBM Promidis, Pomezia, Rome, Italy.
  • Boggio R; IRBM Promidis, Pomezia, Rome, Italy.
  • Padova A; IRBM Promidis, Pomezia, Rome, Italy.
  • Kuhn R; IRBM Promidis, Pomezia, Rome, Italy.
  • Pacifici R; CHDI Management/CHDI Foundation, Los Angeles, California, United States of America.
  • Macdonald D; CHDI Management/CHDI Foundation, Los Angeles, California, United States of America.
  • Schoenfeld RC; CHDI Management/CHDI Foundation, Los Angeles, California, United States of America.
  • Park H; CHDI Management/CHDI Foundation, Los Angeles, California, United States of America.
  • Isas JM; Department of Biochemistry and Molecular Biology, Zilkha Neurogenetic Institute, Keck School of Medicine, University of Southern California, Los Angeles, California, United States of America.
  • Langen R; Department of Biochemistry and Molecular Biology, Zilkha Neurogenetic Institute, Keck School of Medicine, University of Southern California, Los Angeles, California, United States of America.
  • Weiss A; IRBM Promidis, Pomezia, Rome, Italy.
  • Caricasole A; IRBM Promidis, Pomezia, Rome, Italy.
PLoS One ; 9(12): e112262, 2014.
Article en En | MEDLINE | ID: mdl-25464275

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Péptidos / Proteínas Mutantes / Proteínas del Tejido Nervioso Tipo de estudio: Prognostic_studies Límite: Humans Idioma: En Revista: PLoS One Asunto de la revista: CIENCIA / MEDICINA Año: 2014 Tipo del documento: Article País de afiliación: Italia

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Péptidos / Proteínas Mutantes / Proteínas del Tejido Nervioso Tipo de estudio: Prognostic_studies Límite: Humans Idioma: En Revista: PLoS One Asunto de la revista: CIENCIA / MEDICINA Año: 2014 Tipo del documento: Article País de afiliación: Italia