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Polyglutamine expansion affects huntingtin conformation in multiple Huntington's disease models.
Daldin, Manuel; Fodale, Valentina; Cariulo, Cristina; Azzollini, Lucia; Verani, Margherita; Martufi, Paola; Spiezia, Maria Carolina; Deguire, Sean M; Cherubini, Marta; Macdonald, Douglas; Weiss, Andreas; Bresciani, Alberto; Vonsattel, Jean-Paul Gerard; Petricca, Lara; Marsh, J Lawrence; Gines, Silvia; Santimone, Iolanda; Marano, Massimo; Lashuel, Hilal A; Squitieri, Ferdinando; Caricasole, Andrea.
Afiliación
  • Daldin M; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Fodale V; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Cariulo C; IRBM Promidis, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Azzollini L; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Verani M; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Martufi P; IRBM Promidis, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Spiezia MC; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Deguire SM; IRBM Promidis, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Cherubini M; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Macdonald D; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Weiss A; Laboratory of Molecular and Chemical Biology of Neurodegeneration, Brain Mind Institute, Station 19, School of Life Sciences, Ecole Polytechnique Fédérale de Lausanne (EPFL), CH-1015, Lausanne, Switzerland.
  • Bresciani A; Departamento de Ciencias Biomedicas, Facultat de Medicina, Instituto de Neurociencias, Universitat de Barcelona, Barcelona, Spain.
  • Vonsattel JG; CHDI Management/CHDI Foundation, Los Angeles, CA, 90045, USA.
  • Petricca L; IRBM Promidis, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Marsh JL; Evotec AG, Manfred Eigen Campus, Hamburg, Germany.
  • Gines S; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Santimone I; Taub Institute for Research on Alzheimer's disease and the Aging Brain, Columbia University Medical Center, 710 West 168th Street, New York, NY, 10032, USA.
  • Marano M; IRBM Science Park, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Lashuel HA; IRBM Promidis, Via Pontina km 30.600, 00071, Pomezia, Rome, Italy.
  • Squitieri F; Department of Developmental and Cell Biology, University of California, Irvine, 92697, USA.
  • Caricasole A; Departamento de Ciencias Biomedicas, Facultat de Medicina, Instituto de Neurociencias, Universitat de Barcelona, Barcelona, Spain.
Sci Rep ; 7(1): 5070, 2017 07 11.
Article en En | MEDLINE | ID: mdl-28698602

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Péptidos / Enfermedad de Huntington / Expansión de Repetición de Trinucleótido / Proteína Huntingtina Tipo de estudio: Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Sci Rep Año: 2017 Tipo del documento: Article País de afiliación: Italia

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Péptidos / Enfermedad de Huntington / Expansión de Repetición de Trinucleótido / Proteína Huntingtina Tipo de estudio: Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Sci Rep Año: 2017 Tipo del documento: Article País de afiliación: Italia