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Lung function decline is delayed but not decreased in patients with cystic fibrosis and the R117H gene mutation.
Wagener, Jeffrey S; Millar, Stefanie J; Mayer-Hamblett, Nicole; Sawicki, Gregory S; McKone, Edward F; Goss, Christopher H; Konstan, Michael W; Morgan, Wayne J; Pasta, David J; Moss, Richard B.
Afiliación
  • Wagener JS; Department of Pediatrics, University of Colorado, Aurora, CO, USA. Electronic address: jeffrey.wagener@ucdenver.edu.
  • Millar SJ; ICON Clinical Research, San Francisco, CA, USA.
  • Mayer-Hamblett N; US CFF Patient Registry Committee, Bethesda, MD, USA; Department of Pediatrics and Biostatistics, University of Washington, Seattle, WA, USA.
  • Sawicki GS; US CFF Patient Registry Committee, Bethesda, MD, USA; Department of Pediatrics, Harvard Medical School, Boston, MA, USA.
  • McKone EF; Thoracic Medicine, St. Vincent's University Hospital, Dublin, Ireland.
  • Goss CH; US CFF Patient Registry Committee, Bethesda, MD, USA; Department of Medicine, University of Washington, Seattle, WA, USA.
  • Konstan MW; Department of Pediatrics, Case Western Reserve University, Cleveland, OH, USA.
  • Morgan WJ; US CFF Patient Registry Committee, Bethesda, MD, USA; Department of Pediatrics, University of Arizona, Tucson, AZ, USA.
  • Pasta DJ; ICON Clinical Research, San Francisco, CA, USA.
  • Moss RB; Department of Pediatrics, Stanford University, Palo Alto, CA, USA.
J Cyst Fibros ; 17(4): 503-510, 2018 07.
Article en En | MEDLINE | ID: mdl-29100868

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Pruebas de Función Respiratoria / Regulador de Conductancia de Transmembrana de Fibrosis Quística / Fibrosis Quística / Obstrucción de las Vías Aéreas / Pulmón Tipo de estudio: Diagnostic_studies / Etiology_studies / Prognostic_studies Límite: Adolescent / Adult / Child / Female / Humans / Male País/Región como asunto: America do norte Idioma: En Revista: J Cyst Fibros Año: 2018 Tipo del documento: Article

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Pruebas de Función Respiratoria / Regulador de Conductancia de Transmembrana de Fibrosis Quística / Fibrosis Quística / Obstrucción de las Vías Aéreas / Pulmón Tipo de estudio: Diagnostic_studies / Etiology_studies / Prognostic_studies Límite: Adolescent / Adult / Child / Female / Humans / Male País/Región como asunto: America do norte Idioma: En Revista: J Cyst Fibros Año: 2018 Tipo del documento: Article