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Pathological manifestations of Farber disease in a new mouse model.
Beckmann, Nadine; Kadow, Stephanie; Schumacher, Fabian; Göthert, Joachim R; Kesper, Stefanie; Draeger, Annette; Schulz-Schaeffer, Walter J; Wang, Jiang; Becker, Jan U; Kramer, Melanie; Kühn, Claudine; Kleuser, Burkhard; Becker, Katrin Anne; Gulbins, Erich; Carpinteiro, Alexander.
Afiliación
  • Beckmann N; Department of Molecular Biology, University of Duisburg-Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Kadow S; Department of Molecular Biology, University of Duisburg-Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Schumacher F; Department of Molecular Biology, University of Duisburg-Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Göthert JR; Department of Toxicology, Institute of Nutritional Science, University of Potsdam, Arthur-Scheunert-Allee 114-116, D-14558 Nuthetal, Germany.
  • Kesper S; Department of Hematology, University Hospital Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Draeger A; Department of Hematology, University Hospital Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Schulz-Schaeffer WJ; Institute of Anatomy, University of Bern, Baltzerstr. 2, CH-3012 Bern, Switzerland.
  • Wang J; Insitute of Neuropathology, University of the Saarland, Kirrberger Str. 100, D-66421 Homburg, Germany.
  • Becker JU; Department of Pathology and Laboratory Medicine, UC Health University Hospital, 234 Goodman Street, Cincinnati, OH 45219, USA.
  • Kramer M; Institute of Pathology, University Hospital Cologne, Kerpener Straße 62, D-50937 Cologne, Germany.
  • Kühn C; Department of Molecular Biology, University of Duisburg-Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Kleuser B; Department of Molecular Biology, University of Duisburg-Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Becker KA; Department of Toxicology, Institute of Nutritional Science, University of Potsdam, Arthur-Scheunert-Allee 114-116, D-14558 Nuthetal, Germany.
  • Gulbins E; Department of Molecular Biology, University of Duisburg-Essen, Hufelandstraße 55, D-45147 Essen, Germany.
  • Carpinteiro A; Department of Molecular Biology, University of Duisburg-Essen, Hufelandstraße 55, D-45147 Essen, Germany.
Biol Chem ; 399(10): 1183-1202, 2018 09 25.
Article en En | MEDLINE | ID: mdl-29908121

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Modelos Animales de Enfermedad / Lipogranulomatosis de Farber Límite: Animals Idioma: En Revista: Biol Chem Asunto de la revista: BIOQUIMICA Año: 2018 Tipo del documento: Article País de afiliación: Alemania

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Modelos Animales de Enfermedad / Lipogranulomatosis de Farber Límite: Animals Idioma: En Revista: Biol Chem Asunto de la revista: BIOQUIMICA Año: 2018 Tipo del documento: Article País de afiliación: Alemania