[The SAPHO syndrome: a study of 16 cases]. / Síndrome SAPHO: estudio de 16 casos.
Med Clin (Barc)
; 112(2): 61-3, 1999 Jan 23.
Article
em Es
| MEDLINE
| ID: mdl-10065433
ABSTRACT
The SAPHO syndrome is characterized by synovitis, acne, palmo-plantar pustulosis, hyperostosis and osteitis. SAPHO syndrome has been occasionally described in Spain. We present our experience of 16 cases with the SAPHO syndrome diagnosed between 1984-1995. The predominant clinical symptoms were anterior thoracic pain (14 cases), sacroiliac pain (7 cases) and peripheral arthritis (2 cases). Cutaneous involvement was characterized by palmo-plantar pustulosis (8 cases) acne (3 cases) and psoriasis (2 cases). The histocompatibility antigen B27 was negative in all cases. A computerized tomographic study revealed involvement of sterno-costo-clavicular and manubriosternal joints (14 cases) and sacroiliitis (8 cases).
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Bases de dados:
MEDLINE
Assunto principal:
Síndrome de Hiperostose Adquirida
Tipo de estudo:
Diagnostic_studies
/
Observational_studies
Limite:
Adolescent
/
Adult
/
Aged
/
Female
/
Humans
/
Male
/
Middle aged
País/Região como assunto:
Europa
Idioma:
Es
Revista:
Med Clin (Barc)
Ano de publicação:
1999
Tipo de documento:
Article