[Perioperative management of a neonate with aglossia-adactylia syndrome].
Masui
; 50(7): 773-5, 2001 Jul.
Article
em Ja
| MEDLINE
| ID: mdl-11510070
ABSTRACT
Aglossia-adactylia syndrome is a rare disorder characterized by aglossia and deformity of the limbs of variable degree. We managed a 2-day-old neonate with ileojejunal atresia with aglossia-adactylia syndrome. He was scheduled for the repair of the intestinal atresia, gastrostomy and palatal impression taking, under general anesthesia with sevoflurane supplemented with fentanyl. In this case we could achieve tracheal intubation by direct laryngoscopy with cricoid pressure applied, and could manage without any complications. But many of the patients with this syndrome are complicated with cleft palate and micrognathia, and we should be careful of the difficult airway at the induction of general anesthesia and aspiration during perioperative period.
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Bases de dados:
MEDLINE
Assunto principal:
Língua
/
Anormalidades Múltiplas
/
Deformidades Congênitas dos Membros
/
Assistência Perioperatória
Limite:
Humans
/
Male
/
Newborn
Idioma:
Ja
Revista:
Masui
Ano de publicação:
2001
Tipo de documento:
Article