Herlyn-Werner-Wunderlich syndrome: a very rare urogenital anomaly in a teenage girl.
J Emerg Med
; 48(3): e73-5, 2015 Mar.
Article
em En
| MEDLINE
| ID: mdl-25499400
ABSTRACT
BACKGROUND:
Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon variant of Müllerian duct anomalies, consisting of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents in a post-pubertal adolescent or adult woman in whom hematometrocolpos produces a pronounced mass effect and pain on the side of the obstructed hemivagina. CASE REPORT We report the case of a 13-year-old girl who presented to the emergency radiology department with sudden onset of severe pain at the right lower quadrant of the abdomen; imaging confirmed the diagnosis of HWW syndrome. WHY SHOULD AN EMERGENCY PHYSICIAN BE AWARE OF THIS? When unilateral renal agenesis and uterus didelphys coexist, the first thing that the physician should remember is to confirm or refute the presence of a blind vagina for diagnosis of HWW syndrome.Palavras-chave
Texto completo:
1
Bases de dados:
MEDLINE
Assunto principal:
Anormalidades Congênitas
/
Útero
/
Vagina
/
Anormalidades Múltiplas
/
Hidrocolpos
/
Rim
/
Nefropatias
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
Limite:
Adolescent
/
Female
/
Humans
Idioma:
En
Revista:
J Emerg Med
Assunto da revista:
MEDICINA DE EMERGENCIA
Ano de publicação:
2015
Tipo de documento:
Article
País de afiliação:
Turquia