Addison's disease presenting with perimyocarditis.
J Pediatr Endocrinol Metab
; 31(1): 101-105, 2018 01 26.
Article
em En
| MEDLINE
| ID: mdl-29252198
ABSTRACT
BACKGROUND:
Polyglandular autoimmune syndrome (PGA) and eosinophilic granulomatosis with polyangiitis (EGPA) do not seem to represent a coincidental association. CASE PRESENTATION A case of a 15-year-old boy is reported who presented with severe systemic inflammation, perimyocarditis and cardiogenic shock, in whom EGPA was initially suspected and later diagnosed with autoimmune adrenalitis with PGA.CONCLUSIONS:
The severity of the systemic inflammation and perimyocarditis suggests a more widespread autoimmune-mediated process. Autoimmune adrenal insufficiency should be considered in all cases of pericarditis and perimyocarditis, especially when the severity of clinical manifestations exceeds the expected for the severity of the cardiac findings, as timely identification and prompt treatment may be life-saving.Palavras-chave
Texto completo:
1
Bases de dados:
MEDLINE
Assunto principal:
Pericardite
/
Pericárdio
/
Doença de Addison
/
Miocardite
Tipo de estudo:
Etiology_studies
/
Prognostic_studies
Limite:
Adolescent
/
Humans
/
Male
Idioma:
En
Revista:
J Pediatr Endocrinol Metab
Assunto da revista:
ENDOCRINOLOGIA
/
PEDIATRIA
Ano de publicação:
2018
Tipo de documento:
Article
País de afiliação:
Brasil